Polyps in the small intestine have been described in children with PPB and/or DICER1 variation. Generally, these have been seen in individuals from birth to 10 years of age. This can result in intestinal obstruction, and surgery may be required.
Intestinal polyps may present with abdominal pain, constipation, bloody stool and may result in intestinal obstruction.
When intestinal obstruction occurs, surgery may be required.