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PPB Registry
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Resources

  • Judicious DICER1 Testing and Surveillance Imaging Facilitates Early Diagnosis and Cure of Pleuropulmonary Blastoma

  • Temporal order of RNase IIIb and loss-of-function mutations during development determines phenotype in DICER1 syndrome: a unique variant of the two-hit tumor suppression model

  • DICER1 and Associated Conditions: Identification of At-risk Individuals and Recommended Surveillance Strategies

  • Pleuropulmonary Blastoma: A Report on 350 Central Pathology–Confirmed Pleuropulmonary Blastoma Cases by the International Pleuropulmonary Blastoma Registry

  • DICER1-related Sertoli-Leydig cell tumor and gynandroblastoma: Clinical and genetic findings from the International Ovarian and Testicular Stromal Tumor Registry
Go to PubMed
Go to ClinicalTrials.gov

Resources for health professionals

  • Help with any questions related to PPB and other DICER1-related cancers
  • Testing and surveillance guidelines to detect PPB and other DICER1-related cancers in their earliest and most curable form
  • Schemas, roadmaps, and schedules
  • Further information regarding treatment of Types I, II, III, and Ir PPB
  • Our publication of 350 cases

Organizations with additional resources

  • Children’s Minnesota
  • GeneReviews
  • International Ovarian and Testicular Stromal Tumor Registry (OTST)
  • National Cancer Institute
  • National Organization for Rare Diseases
  • Pine Tree Apple Classic Fund

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The International Pleuropulmonary Blastoma/DICER1 Registry
Children’s Minnesota
910 E. 26th St., Ste. LL08
Minneapolis, MN 55404

Phone: 612-813-7121
Fax: 612-813-7108
Email: [email protected]


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Copyright ©2025 The International PPB/DICER1 Registry. All rights reserved. Data and recommendations on this site are conscientiously presented but some are unpublished observations and have not undergone peer review. Consultation with the Registry is encouraged to clarify any topics. The International PPB/DICER1 Registry advises caution in the citation of website information.