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The International Pleuropulmonary Blastoma Registry
The International Pleuropulmonary Blastoma Registry
The Genetics of PPB

Critical Issues


Constitutional & Familial Issues: Genetics of PPB:


A Very Rare Disease: Enrolling Patients in the Registry


Cerebral Metastases in PPB


Genetic Study of PPB


PPB Associated with Cystic Nephroma and Other Renal Tumors


Type I PPB: Treatment Issues


Type II and III THERAPY RECOMMENDATION CHANGE

Join Our PPB Study

Whats New

04/09/2010
2010 PPB FAMILY WEEKEND IN WASHINGTON DC

02/15/2007
THERAPY CHANGE: PPB Types II and III

11/15/2006
PPB, Cystic Nephroma & Small Bowel Polyps

10/01/2005
Genetic Study in PPB - PPB Tissue Bank

Literature Sources
Please use the search field or click on a focus category to locate a specific literature source.
298 Search Results :
2010 Katzenstein HM, Petricca S, Ricketts R, Wasilewski-Master K, Powell C, Rapkin L, George B, Woods WG, Olson TA.
Intracavitary cisplatin therapy for pediatric malignancies.
Pediatr Blood Cancer
55:452-56.
Number of Cases: 2
Focus Categories: general PPB-related topic 
2010 Burge D, Wheeler R.
Increasing incidence of detection of congenital lung lesions [Letter to Ed].
Pediatr Pulmonol
45:103
Number of Cases: 0
Focus Categories: lung cyst 
2010 Priest JR, Jaffe A.
Increasing incidence of detection of congenital lung lesions [Reply].
Pediatr Pulmonol
45:104.
Number of Cases: 0
Focus Categories: lung cyst  Registry publication 
2010 Reichman M, Kovanlikaya A, Mathew S, Beneck D, Brill PW.
Pulmonary blastoma in a neonate: a lesion distinct from pleuropulmonary blastoma with unique cytogenetic features.
Pediatr Radiol
40(3):366-70.
Number of Cases: 0
Focus Categories: general PPB-related topic 
2010 Goel P, Panda S, Srinivas M, Kumar D, Seith A, Ahuja A, Sarkar C, Chowdhury S, Agarwala S.
Pleuropulmonary blastoma with intrabronchial extension.
Pediatr Blood Cancer
54(7):1026-1028.
Number of Cases: 1
Focus Categories: pathology discussion  imaging of PPB 
2010 Shaheen IS, Fitzpatrick M, Brownlee K, Bhuskute N, Elliott M, Powis M, Ahmad N, Tyerman K.
Bilateral progressive cystic nephroma in a 9-month old boy requiring renal replacement therapy.
Pediatr Nephrol
[in press].
Number of Cases: 1
Focus Categories: cystic nephroma 
2010 Priest JR, Andic D, Arbuckle S, Gonzalez-Gomez I, Hill DA Williams G.
Great vessel and cardiac extension and tumor embolism in pleuropulmonary blastoma - a report from the International Pleuropulmonary Blastoma Registry
Pediatric Blood and Cancer
in press
Number of Cases: 11
Focus Categories: imaging of PPB  macrovascular invasion/embolism  neo-adjuvant chemotherapy  Registry publication  SVC syndrome 
2010 Cross SF, Arbuckle S, Priest JR, Marshall G, Charles A, Dalla Pozza, L.
Familial Pleuropulmonary Blastoma in Australia
Pediatric Blood and Cancer
in press
Number of Cases: 4
Focus Categories: Registry publication  familial/constitutional  cystic nephroma 
2010 Schultz KA, Williams G, Hill D, Dehner LP, Priest J.
Ovarian tumors in association with pleuropulmonary blastoma: a new manifestation of the PPB Tumor syndrome [Abstract].
Pediatr Blood Cancer
54(6):850
Number of Cases: 8
Focus Categories: Registry publication  familial/constitutional 
2010 Hill DA, Wang JD, Schoettler P, Dehner L, Ivanovich J, Bracamontes D, Williams G, Messinger Y, Goodfellow PJ, Priest J.
Germline DICER1 mutations are common in both hereditary and presumed sporadic pleuropulmonary blastoma [Abstract].
Lab Invest
90:311
Number of Cases: 68
Focus Categories: Registry publication  familial/constitutional  DICER1 mutation 
2010 Cummings NM, Desai S, Thway K, Stewart S, Hill DA, Priest JR, Nicholson AG, Rintoul RC.
Cystic primary pulmonary synovial sarcoma presenting as recurrent pneumothorax: report of four cases.
Am J Surg Pathol
34(8):1176-79.
Number of Cases: 4
Focus Categories: Registry publication  adult 
2010 Bahubeshi A, Bal N, Rio Frio T, Hamel N, Pouchet C, Yilmaz A, Bouron-Dal Soglio D, Williams GM, Tischkowitz M, Priest JR, Foulkes WD.
Bahubeshi A, Bal N, Rio Frio T, Hamel N, Germline DICER1 mutations and familial cystic nephroma.
J Med Genet
[in press]
Number of Cases: 4
Focus Categories: cystic nephroma  DICER1 mutation  familial/constitutional 
2010 Priest JR, Williams GM, Mize WA, Dehner LP.
Priest JR, Williams GM, Mize WA, Dehner LP. Nasal chondromesenchymal hamartoma in children with pleuropulmonary blastoma: a report from the International Pleuropulmonary Blastoma Registry.
Int J Pediatr Otorhinolaryngol
[in press]
Number of Cases: 4
Focus Categories: familial/constitutional  Registry publication 
2010 Chen S, Wang S, Gao J, Zhang S.
Pleuropulmonary blastoma: a clinicopathological analysis.
Chin J Lung Cancer
13(5):550-53.
Number of Cases: 5
Focus Categories: pathology discussion 
2009 Schiavetti A, Indolfi P, Hill DA, Priest JR
Primary pulmonary rhabdomyosarcoma in childhood: clinico-biologic features in two cases with review of the literature--erratum
Pediatr Blood Cancer
52(1):146.
Number of Cases: 2
Focus Categories: pathology discussion  Registry publication 
2009 Priest JR, Williams GM, Hill DA, Dehner LP, Jaffé A.
Pulmonary cysts in early childhood and the risk of malignancy.
Pediatr Pulmonol
44(1):14-30.
Number of Cases: 0
Focus Categories: Type I PPB  Registry publication  major review  lung cyst  imaging of PPB  familial/constitutional  cyst management 
2009 Corapcioglu F, Lima T, Aksu G, Inan N, Deveci M, Gurbuz Y, Topcu S.
A case report with type II pleuropulmonary blastoma: successful treatment with surgery and chemotherapy.
Turk J Pediatr
51:78-81.
Number of Cases: 1
Focus Categories: bilateral  lung cyst 
2009 Hill DA, Ivanovich J, Priest JR, Gurnett CA, Dehner LP, Desruisseau D, Jarzembowski JA, Wikenheiser KA, Suarez BK, Whelan AJ, Williams G, Bracamontes B, Messinger Y, Goodfellow PJ.
Inherited DICER1 mutations in familial pleuropulmonary blastoma [abstract].
Annual Meeting for American Association for Cancer Research
Abstract LB-91.
Number of Cases: 11
Focus Categories: Registry publication  familial/constitutional  DICER1 mutation 
2009 Wu X, Crump M, Hannon G, Millar S.
Epithelial Dicer is required for postnatal mammary gland development and stem cell maintenance [abstract].
Proceedings of the 100th Annual Meeting of the American Association for Cancer Research
AACR; 2009. Abstract nr 1937.
Number of Cases: 0
Focus Categories: DICER1 mutation 
2009 Kirsch S, Vokuhl C, Leuschner I, Int-Veen C, Dantonello TM, Schuck A, Bielack SS, Klingebiel T, Koscielniak E.
The importance of multimodal treatment in pleuropulmonary blastoma-experience of the cooperative Weichteilsarkom Study Group (CWS) [Abstract].
Annual Meeting for American Association for Cancer Research
O.105:48.
Number of Cases: 19
Focus Categories: CNS metastasis  general PPB-related topic 
2009 Dehner LP.
USCAP Specialty Conference, case 4: Sertoli cell tumor of the ovary.
Pediatr Dev Pathol
In Press
Number of Cases: 1
Focus Categories: familial/constitutional  pathology discussion  Registry publication 
2009 Hill DA, Ivanovich J, Priest JR, Gurnett CA, Dehner LP, Desruisseau D, Jarzembowski JA, Wikenheiser-Brokamp KA, Suarez BK, Whelan AJ, Williams G, Bracamontes D, Messinger Y, Goodfellow PJ.
DICER1 Mutations in Familial Pleuropulmonary Blastoma.
Science
325:965
Number of Cases: 11
Focus Categories: Registry publication  molecular studies  major review  familial/constitutional  DICER1 mutation 
2009 McCarthy, N.
Non-coding RNA: Dicing with lung cancer.
Nat Rev Cancer
9(8):532.
Number of Cases: 0
Focus Categories: DICER1 mutation 
2009 Carthew RW, Sontheimer EJ
Origins and mechanisms of miRNAs and siRNAs.
Cell
136(4):642-55.
Number of Cases: 0
Focus Categories: DICER1 mutation 
2009 Walsh S, Wood AE, Greally P.
Pleuropulomnary blastoma Type I following resection of incidentally found congenital lobar emphysema.
Ir Med J
102(7): 230.
Number of Cases: 1
Focus Categories: cyst management 
2009 Ohta Y, Fujishima M, Hasegawa H, Kosumi T, Yonekura T.
High therapeutic effectiveness of postoperative irinotecan chemotherapy in a typical case of radiographically and pathologically diagnosed pleuropulmonary blastoma.
J Pediatr Hematal Oncol
31(5):355-58.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2009 Chadli-Debbiche A, Ben Brahim E, Jouini R, Labbene N, Sayed S, Ben Ayed M, Kaabar N.
Pleuropulmonary blastoma: cystic tumour misdiagnosed as an emphysematous bulla.
RespMedCME
[in press]
Number of Cases: 1
Focus Categories: pathology discussion 
2009 Shi YC, Tang LF, Chen ZM, Du LZ.
Pleuropulmonary blastoma in an infant.
Indian J Pediatr
76(9):948-9.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2009 Kumar M, Pester RE, Chen CY, Lane K, Chin C, Lu J, Kirsch DG, Golub TR, Jacks T.
Dicer1 functions as a haploinsufficient tumor suppressor.
Genes Dev
23(23):2700-4.
Number of Cases: 0
Focus Categories: DICER1 mutation 
2009 Lambertz I, Nittner D, Mestdagh P, Denecker G, Vandesompele J, Dyer MA, Marine JC.
Monoallelic but not biallelic loss of Dicer1 promotes tumorigenesis in vivo.
Cell Death Differ
17(4):633-41
Number of Cases: 0
Focus Categories: DICER1 mutation 
2009 Taskinen S, Lohi J, Kivisaari R, Fagerholm R, Rintala R, Taskinen M.
Segmental cystic kidney tumours in children.
Scand J Urol Nephrol
43:476-81.
Number of Cases: 1
Focus Categories: cystic nephroma 
2008 Oue T, Inoue M, Kubota A, Kuwae Y, Kawa K.
Pediatric thyroid cancer arising after treatment for pleuropulmonary blastoma.
Pediatr Blood Cancer
50(4):901-2.
Number of Cases: 1
Focus Categories: familial/constitutional 
2008 Hill DA, Jarzembowski JA, Priest JR, Williams G, Schoettler P, Dehner LP.
Type I pleuropulmonary blastoma: pathology and biology study of 51 cases from the International Pleuropulmonary Blastoma Registry.
Am J Surg Pathol
32(2):282-295
Number of Cases: 51
Focus Categories: Type I PPB  Registry publication  pathology discussion 
2008 Rome A, Gentet JC, Coze C, Andre N.
Pediatric thyroid cancer arising as a fourth cancer in a child [Letter].
Pediatr Blood Cancer
50(5):1081
Number of Cases: 1
Focus Categories: familial/constitutional 
2008 Herman TE, Siegel MJ
Neonatal pleuropulmonary blastoma, type 1.
J Perinatol
28(1):82-4.
Number of Cases: 1
Focus Categories: imaging of PPB  Type I PPB 
2008 Libretti L, Ciriaco P, Casiraghi M, Arrigoni G, Zannini P.
Pleuropulmonary blastoma in the area of a diagnosed congenital lung cyst.
Ann Thorac Surg
85:658-60.
Number of Cases: 1
Focus Categories: cyst management 
2008 Balassy C, Kulemann V, Hormann M.
Malignant pulmonary tumors in children.
Radiologe
48(10):955-61
Number of Cases: 1
Focus Categories: imaging of PPB 
2008 Gupta K, Vankalakunti M, Das A, Marwaha RK.
An autopsy report of a rare pediatric lung tumor: pleuropulmonary blastoma.
Indian J Pathol Microbiol
51(2):225-7
Number of Cases: 1
Focus Categories: general PPB-related topic  pathology discussion 
2008 Gutweiler JR, LaBelle J, Suh MY, Misra MV, Ahmed M, Lee EY, Vargas SO, Kim HB, Weldon CB.
A familial case of pleuropulmonary blastoma.
Eur J Pediatr Surg
18(3):192-4
Number of Cases: 2
Focus Categories: familial/constitutional 
2008 Fosdal MB
Pleuropulmonary blastoma
J Pediatr Oncol Nurs
25(6):295-302.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2008 Chang HL, Rosenberg AE, Friedmann AM, Ryan DP, Masiakos PT.
Primary pulmonary rhabdomyosarcoma in a 5-month old boy.
J Pediatr Hematol Oncol
30:461-3.
Number of Cases: 0
Focus Categories: general PPB-related topic 
2008 Agarwal AK, Das S, Agarwal A, Ghosh D, Chaterjee N, Pal MS
Pleuropulmonary blastema with cystic nephroma - a rare presentation and surgical dilemma.
Indian J Pediatr
Dec 4 [Epub ahead of print]
Number of Cases: 1
Focus Categories: cystic nephroma 
2008 Griffin N, Devaraj A, Goldstraw P, Bush A, Nicholson AG, Padley S.
CT and histopatholgical correlation of congenital cystic pulmonary lesions: a common pathogenesis?
Clin Radiol
63(9):995-1005.
Number of Cases: 4
Focus Categories: imaging of PPB 
2008 Igune VLR, Cetti AKO, Traibel LG, Estevan M.
Blastoma pleuropulmonar en un preescolar. Una causa poco frecuente de tumor pulmonar en el nino.
Arch Pediatr Urug
79(1):32-7.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2008 MutPons R, Velilla M, SanguesaNebot C, RamirezLatorre O.
[Pleuropulmonary blastoma in children: imaging findings and clinical patterns].
Radiologia
50(6):489-94.
Number of Cases: 3
Focus Categories: imaging of PPB 
2008 Khatami A, Gharib A, Hadale M, Hadaie F.
Pleuro-pulmonary blastoma in a 4-year-old child.
Iran J Radiol
5(3):159-62.
Number of Cases: 1
Focus Categories: cystic nephroma 
2008 Shaheen I, Tyeman K, Fitzpatrick M, Finlay E, Feather S, Powls M, Brownlee K, Elliott M.
Case report of renal and lung cysts, a unique association [Abstract].
Pediatr Nephrol
23:1651.
Number of Cases: 1
Focus Categories: cystic nephroma 
2007 Indolfi P, Bisogno G, Casale F, Cecchetto G, De Salvo G, Ferrari A, Donfrancesco A, Donofrio V, Martone A, Di Martino M, Di Tullio MT.
Prognostic factors in pleuro-pulmonary blastoma.
Pediatr Blood Cancer
48(3):318-23.
Number of Cases: 22
Focus Categories: major review 
2007 Aljehani YM, Elbaz AM, Moghazy KM, Alardi AA, Montaser AA, El-Ghoneimy YF.
Pleuropulmonary blastoma. A rare childhood malignancy.
Saudi Med J
28(9):1443-5.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2007 Ashley RA, Reinberg YE.
Familial multilocular cystic nephroma: a variant of a unique renal neoplasm.
Urology
178:1813-5.
Number of Cases: 0
Focus Categories: familial/constitutional  cystic nephroma 
2007 Priest JR, Magnuson J, Williams GM, Abromowitch M, Byrd R, Sprinz P, Finkelstein M, Moertel CL, Hill DA.
Cerebral metastasis and other central nervous system complications of pleuropulmonary blastoma.
Pediatr Blood Cancer
49(3):266-73.
Number of Cases: 39
Focus Categories: Registry publication  major review  CNS metastasis 
2007 Vargas SO, Legallo RD, Pascacio JM, Moore J, Qualman SJ.
Primary pediatric intrathoracic primitive sarcomas: critical reappraisal of the spectrum of pleuropulmonary blastoma based on review of 63 patients [Abstract].
Annual Mtg Society for Pediatr Pathol
Mar.
Number of Cases: 42
Focus Categories: pathology discussion 
2007 Pai S, Eng HL, Lee SY, Hsaio CC, Huang WT, Huang SC, Hill DA, Dehner LP, Priest JR.
Correction: Pleuropulmonary blastoma, not rhabdomyosarcoma in a congenital lung cyst [Letter to the Editor].
Pediatr Blood Cancer
Mar;48(3):370-1.
Number of Cases: 1
Focus Categories: cyst management  lung cyst  pathology discussion  Registry publication  Type I PPB 
2007 Johnson C, Nagaraj U, Esguerra J, Wasdahl D, Wurzbach D.
Nasal chondromesenchymal hamartoma: radiographic and histopathologic analysis of a rare pediatric tumor.
Pediatr Radiol
37:101-4
Number of Cases: 1
Focus Categories: familial/constitutional 
2007 Hill DA, Dishop MK, McKay EM, Langston C, Priest JR, Dehner LP.
Immature interstitial mesenchymal tumor (IIMT): a distinctive new entity of the infant lung [Abstract].
Mod Pathol
20:279-300.
Number of Cases: 4
Focus Categories: pathology discussion  Registry publication 
2007 Hill DA, Jarzembowski JA, Lennerz JK, Spence D, Schoettler P, Priest JR, Williams G, Dehner LP.
Histologic features of Type I pleuropulmonary blastoma (PPB) [Abstract].
Annual Meeting of the Society for Pediatric Pathology
Mar.
Number of Cases: 41
Focus Categories: pathology discussion  Registry publication 
2007 Lennerz JK, Jarzembowski JA, Spence D, Schoettler P, Dehner LP, Hill DA.
Diagnostic features of pleuropulmonary blastoma (PPB) are absent in congenital cystic adenomatoid malformation [Abstract].
Annual Meeting of the Society for Pediatric Pathology
Mar.
Number of Cases: 57
Focus Categories: pathology discussion  Registry publication 
2007 Mechoulan A, Leclair MD, Yvinec M, Philippe HJ, Winer N.
Pleuropulmonary blastoma: a case of early neonatal diagnosis through antenatal scan screening.
Gynecol Obstet Fertil
35(5):437-41
Number of Cases: 1
Focus Categories: imaging of PPB 
2007 Orazi C, Inserra A, Schingo PMS, De Sio L, Cutrera R, Boldrini R, Malena S.
Pleuropulmonary blastoma, a distinctive neoplasm of childhood: report of three cases.
Pediatr Radiol
27:227-44.
Number of Cases: 3
Focus Categories: CNS metastasis  imaging of PPB 
2007 Shivastava R, Saha A, Mehera B, Batra P, Gagane NM.
Pleuropulmonary blastoma: transition from type I (cystic) to type III (solid).
Singapore Med J
48(7):e190-2.
Number of Cases: 1
Focus Categories: Type I PPB  type progression 
2007 Zuker NB, Dietl CA, Kenna S, Fischer EG, Gardner D.
Unusual survival of an adult with pleuropulmonary blastoma and neurofibromatosis.
J Thorac Cardiovasc Surg
134(2):541-2.
Number of Cases: 1
Focus Categories: adult  familial/constitutional 
2007 Geiger J, Walter K, Uhl M, Bley TA, Juttner E, Brink I, Kirschbaum A, Kontny U.
Imaging findings in a 3-year-old girl with Type III pleuropulmonary blastoma.
In Vivo
21:1119-22.
Number of Cases: 1
Focus Categories: imaging of PPB 
2007 de Krijger RR, Claessen SMH, van der Ham F, van Unnik AJM, Hulsbergen-van de Kaa CA, van Leuven L, van Noesel M, Speel EJM.
Gain of chromosome 8q is a frequent finding in pleuropulmonary blastoma.
Mod Pathol
20(11):1191-9.
Number of Cases: 5
Focus Categories: cytogenetics 
2007 David M, Bosdure E, deLagausie P, Rome A, Gorincour G, Chabrol B, Dubus JC.
Kystic pleuropulmonary blastoma fortuitly discovered in an infant.
Arch Pediatr
Oct 10:Epub
Number of Cases: 1
Focus Categories: Type I PPB 
2007 Nur S, Badr R, Sandoval C, Brudniki A, Yeh A.
Syndromic presentation of a pleuropulmonary blastoma associated with congenital cystic adenomatoid malformation. A case report.
J Pediatr Surg
42(10):1772-5.
Number of Cases: 1
Focus Categories: ASCR - PBSCT  CNS metastasis  cyst management  lung cyst 
2007 Watanabe M, Kaneko M, Yukihiro T, Sumi K, Yasuhisa U, Takashi F, Takashi S, Kiyoshi O, Yuzuru K, Tatsuo I.
Further surgical treatment strategy for pediatric cancers management of ruptured massive type III pleuropulmonary blastoma: A case report.
Jpn J Pediatr Surg
39(2):217-22.
Number of Cases: 1
Focus Categories: ASCR - PBSCT 
2007 Bradnock TJ, MacKinlay GA, McKenzie K.
Thoracoscopic lobectomy for symptomatic CCAM in a five month old infant: a cautionary tale from the patholgist [Abstract].
J Laparoendosc Adv Surg Tech
17:547.
Number of Cases: 1
Focus Categories: Type I PPB 
2007 Belcher E, Lawson MH, Nicholson AG, Davison A, Goldstraw P.
Congenital cystic adenomatoid malformation presenting as in-flight systemic air embolisation.
Eur Respir J
30:801-4.
Number of Cases: 1
Focus Categories: Type I PPB 
2006 Stefanaki K, Boman F, Stassinopoulou A, Williams GM, Fournet JC, Bouron-Dal Soglio D, Chauvenet A, Hill A, Messinger Y, Priest JR.
Association of pleuropulmonary blastoma with cystic nephroma and small bowel polyp: case report and data from the International Pleuropulmonary Blastoma Registry [Abstract].
Virchows Arch
448:692.
Number of Cases: 2
Focus Categories: Registry publication  cystic nephroma 
2006 Vargas SO, Korpershoek E, Kozakewich HP, Krijger RR, Fletcher JA, Perez-Atayde AR.
Cytogenetic and p53 profiles in congenital cystic adenomatoid malformation: insights into its relationship with pleuropulmonary blastoma.
Pediatr Dev Pathol
9(3):190-5.
Number of Cases: 2
Focus Categories: Type I PPB  pathology discussion  molecular studies 
2006 Miniati DN, Chintagumpala M, Langston C, Dishop MK, Olutoye OO, Nuchtern JG, Cass DL.
Prenatal presentation and outcome of children with pleuropulmonary blastoma.
J Pediatr Surg
41:66-71.
Number of Cases: 10
Focus Categories: bilateral  lung cyst  cyst management  Type I PPB 
2006 Muwakkit SA, Rodriguez-Galindo C, El Samra AI, Khoury R, Akel SR, Mroueh S, Razzouk B, Abboud MR.
Primary malignant peripheral nerve sheath tumor of the lung in a young child without neurofibromatosis type I.
Pediatr Blood Cancer
47(5):636-8.
Number of Cases: 0
Focus Categories: general PPB-related topic 
2006 Rubinas T, Manera R, Newman B, Picken MM.
Pneumothorax and pulmonary cyst in a 2-year-old child.
Arch Pathol Lab Med
130(4):e47-9.
Number of Cases: 1
Focus Categories: lung cyst 
2006 Bouron-Dal Soglio D, Harvey I, Yazbeck S, Rypens F, Oligny LL, Fournet JC.
An association of pleuropulmonary blastoma and cystic nephroma: possible genetic association.
Pediatr Dev Pathol
9(1):61-64.
Number of Cases: 1
Focus Categories: cystic nephroma 
2006 Priest JR, Hill DA, Williams GM, Moertel CM, Messinger Y, Finkelstein MJ, Dehner LP.
Type I pleuropulmonary blastoma: A report from the International Pleuropulmonary Blastoma Registry.
J Clin Oncol
24:4492-8.
Number of Cases: 38
Focus Categories: Type I PPB  Registry publication  major review  cyst management 
2006 Boman F, Hill DA, Williams GM, Chauvenet A, Fournet JC, BouronDalSoglio D, Messinger Y, Priest JR.
Familial association of pleuropulmonary blastoma with cystic nephroma and other renal tumors: a report from the International Pleuropulmonary Blastoma Registry.
J Pediatr
149(6):850-4.e2.
Number of Cases: 18
Focus Categories: Registry publication  major review  familial/constitutional  cystic nephroma 
2006 D'Angelo P, Manzo V, Venezia S, Alaggio R, Siracusa F.
Pleuropulmonary blastoma: a differential diagnosis of chronic cough. Long-term survival after multimodal aggressive therapy.
Ital J Pediatr
32:122-5.
Number of Cases: 1
Focus Categories: neo-adjuvant chemotherapy 
2006 Hill DA, Williams GM, Finkelstein MJ, Serrano MF, Dehner LP, Priest JR.
Significance of histologic type and anaplasia in pleuropulmonary blastoma [Abstract].
Lab Invest
86(Suppl):212-27.
Number of Cases: 116
Focus Categories: pathology discussion  Registry publication 
2006 Horner JD, Jeannes AM, Guillerman RP, Miniati DN, Dishop MK, Cass DL.
Cystic pleuropulmonary blastoma: an imaging mimic of congenital cystic adenomatoid malformation. [Abstract].
Pediatr Radiol
36(S13):68.
Number of Cases: 5
Focus Categories: imaging of PPB 
2006 Yuksel S, Ekim M, Fitoz S, Soygur T, Sertcelik A, Percinel S, Acar B, Ozcakar ZB, Comba A, Yalcinkaya F.
The association of cystic nephroma with pulmonary sequestration: is it a coincidence or not?
Pediatr Nephrol
21:1041-44.
Number of Cases: 0
Focus Categories: cystic nephroma  general PPB-related topic  major review 
2006 Scott RH, Stiller CA, Walker L, Rahman N.
Syndromes and constitutional chromosomal abnormalities associated with Wilms tumour.
J Med Genet
43:705-15.
Number of Cases: 0
Focus Categories: cystic nephroma  cytogenetics  general PPB-related topic 
2006 Quilichini B, Andre N, Bouvier C, Chrestian MA, Rome A, Intagliata D, Coze C, Lena G, Zattara H.
Hidden chromosomal abnormalities in pleuropulmonary blastomas identified by multiplex FISH.
BMC Cancer
6:4 [e-journal].
Number of Cases: 2
Focus Categories: cytogenetics  molecular studies 
2006 Chetcuti PAJ, Crabbe DCG.
CAM lungs: the conservative approach [Letter].
Arch Dis Child Fetal Neonatal Ed
91:F463-4.
Number of Cases: 0
Focus Categories: cyst management 
2006 Jaffe A, Chitty LS.
Congenital Cystic adenomatoid malformations may not require surgical intervention [Letter}.
Arch Dis Child Fetal Neonatal Ed
91:F464.
Number of Cases: 0
Focus Categories: cyst management 
2006 Al-Backer N, Puligandla PS, Su W, Anselmo M, Laberge JM.
Type I pleuropulmonary blastoma in a 3-year-old male with a cystic lung mass.
J Pediatr Surg
41:E13-E15.
Number of Cases: 1
Focus Categories: cyst management  lung cyst 
2006 Taube JM, Griffin CA, Yonescu R, Morsberger L, Argani P, Askin FB, Batista DAS
Pleuropulmonary blastoma: cytogenetic and spectral karyotype analysis.
Pediatr Dev Pathol
9:453-61.
Number of Cases: 2
Focus Categories: cytogenetics  molecular studies 
2006 Robinson PD, Lord DJE, DallaPozza LD, Harvey JG, VanAsperen PP.
Complicated "pneumonia".
J Paediatr Child Health
42(1-2):62-4.
Number of Cases: 1
Focus Categories: imaging of PPB 
2006 Kaneko H, Isogai K, Kondo M, Hosoi K, Asano T, Funato M, Kondo N.
Autologous peripheral blood stem cell transplantation in a patient with relapsed pleuropulmonary blastoma.
J Pediatr Hematol Oncol
28(6):383-85.
Number of Cases: 1
Focus Categories: ASCR - PBSCT 
2006 Buyukavci M, Atlas S, Salman B, Eren S.
An aggressive childhood tumor mimicking pleural empyema: pleuropulmonary blastoma.
J Pediatr Hematol Oncol
28(4):257-9.
Number of Cases: 1
Focus Categories: imaging of PPB 
2006 Tamura S, Kanaya Y, Tsukahara H, Tanizawa A, Mayumi M, Imamura Y.
Extension of a pleuropulmonary blastoma into the left atrium.
J Jpn Pediatr Soc
110(12):1671-5.
Number of Cases: 1
Focus Categories: ASCR - PBSCT 
2006 Harris KS, Zhang Z, McManus MT, Harfe BD, Sun X.
Harris KS, Zhang Z, McManus MT, Harfe BD, Sun X. Dicer function is essential for lung epithelium morphogenesis.
PNAS
103(7):2208-13
Number of Cases: 0
Focus Categories: DICER1 mutation  general PPB-related topic 
2006 Hammond SM.
MicroRNAs as oncogenes.
Curr Opin Genet Dev
16:4-9.
Number of Cases: 0
Focus Categories: DICER1 mutation 
2006 Jin SC, Cho DS, Song JH.
Fatal aortic tumor embolism presenting as acute paraplegia.
J Korean Neurosurg Soc
39:72-74.
Number of Cases: 1
Focus Categories: macrovascular invasion/embolism 
2006 Park II, Lee EB.
Pleuropulmonary blastoma in lung.
Korean J Thorac Cardiovasc Surg
39(9):722-24.
Number of Cases: 1
Focus Categories: imaging of PPB  pathology discussion  Type I PPB 
2005 Dehner LP.
Beware of "degenerating" congenital pulmonary cysts [Letter to the Editor].
Pediatr Surg Int
21:123-4
Number of Cases: 4
Focus Categories: cyst management  cystic nephroma  pathology discussion  Registry publication 
2005 Priest JR, Messinger Y, Finkelstein MJ, Williams GM, Hill DA, Dehner LP, Moertel CL.
Treatment modality vs outcome in Type I pleuropulmonary blastoma (PPB) - Results from The PPB Registry [abstract].
Pediatr Blood Cancer
44(6):544
Number of Cases: 33
Focus Categories: Registry publication  Type I PPB 
2005 Bal N, Kayaselcuk F, Polat A, Bolat F, Yilmaz Z, Tuncer I.
Familial cystic nephroma in two siblings with pleuropulmonary blastoma.
Pathol Oncol Res
11(1): 53-6.
Number of Cases: 1
Focus Categories: cystic nephroma  familial/constitutional 
2005 Hill DA.
USCAP Specialty Conference, case 1: Type I Pleuropulmonary blastoma.
Pediatr Dev Pathol
8:77-84
Number of Cases: 1
Focus Categories: cystic nephroma  major review  pathology discussion  Registry publication 
2005 Duan M, Wang L, Cao Y, Li Z, Yang W, Rao X, Xiao K.
Results of surgical treatment of congenital cystic lung disease.
Thorac Cardiov Surg
53:61-4.
Number of Cases: 0
Focus Categories: lung cyst  general PPB-related topic 
2005 Indolfi P, Casale F, Bisogno G, Cecchetto G, Ferrari A, Perilongo G, Martone A, Donofrio V, Santoro N, Mazzarino I, Riccardi R, DiMartino M, DiTullio MT.
Pleuropulmonary blastoma after cystic malformations: a better prognosis? [Abstract].
Pediatr Blood Cancer
45(4):452-3.
Number of Cases: 22
Focus Categories: lung cyst  cyst management 
2005 Li H, Sun GQ, Zeng Q, He LJ.
CT features of pleuropulmonary blastoma in children.
Chin J Radiol
39(5):513-6.
Number of Cases: 10
Focus Categories: imaging of PPB  major review 
2005 Kirsch S, Leuschner I, Int-Veen C, Dantonello T, Brecht IB, Schuck A, Bielack S, Klingebiel T, Koscielniak E, Treuner J.
Sixteen children with pleuropulmonary blastoma - results of the German Cooperative Soft Tissue Sarcoma Group [Abstract].
Sarcoma
;9:88
Number of Cases: 16
Focus Categories: lung cyst  CNS metastasis  bilateral  ASCR - PBSCT 
2005 Naffaa LN, Donnelly LF.
Imaging findings in pleuropulmonary blastoma.
Pediatr Radiol
35:387-91.
Number of Cases: 4
Focus Categories: imaging of PPB 
2005 Pai S, Eng HL, Lee SY, Hsiao CC, Huang WT, Huang SC.
Rhabdomyosarcoma arising within congenital cystic adenomatoid malformation.
Pediatr Blood Cancer
45(6):841-5.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2005 Pinarli FG, Oguz A, Karadeniz C, Memis L, Poyraz A.
Type II pleuropulmonary blastoma responsive to multimodal therapy.
Pediatr Hematol Oncol
22(1):71-6.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2005 Sodhi KS, Suri S, Samujh R, Rao KLN, Vaiphei K, Saxena AK.
Bilateral multilocular cystic nephromas: a rare occurrence.
Br J Radiol
78:450-2.
Number of Cases: 0
Focus Categories: cystic nephroma  general PPB-related topic 
2005 Serrano MF, Dehner LP, Williams GM, Priest JR, Hill DA.
Histologic predictors of central nervous system metastasis in pleuropulmonary blastoma: a pilot study [Abstract].
Mod Pathol
18:303.
Number of Cases: 35
Focus Categories: survival of CNS metastasis  Registry publication  pathology discussion  CNS metastasis 
2005 Piastra M, Ruggiero A, Caresta E, Chiaretti A, Pulitano S, Polidori G, Riccardi R.
Life-threatening presentation of mediastinal neoplasms: report on 7 consecutive pediatric patients.
Am J Emerg Med
23:76-82.
Number of Cases: 2
Focus Categories: lung cyst 
2005 Boldrini R, Devito R, Diomedi-Camassei F, Francalanci P, Inserra A, Boglino C, Donfrancesco A, Jenkner A, Callea F.
Pulmonary blastomas of childhood: histologic, immunohistochemical, ultrastructural aspects and therapeutic considerations.
Ultrastruct Pathol
29(6):493-501.
Number of Cases: 6
Focus Categories: molecular studies  pathology discussion 
2005 Bisogno G, Ferrari A, Bergeron C, Scagnellato A, Prete A, Alaggio R, Casanova M, D\'Angelo P, Di Cataldo A, Carli M.
The IVADo regimen - A pilot study with ifosfamide, vincristine, actinomycin D, and doxorubicin in children with metastatic soft tissue sarcoma: a pilot study on behalf of the European pediatric soft tissue sarcoma study group.
Cancer
103(8):1719-24.
Number of Cases: 0
Focus Categories: general PPB-related topic 
2005 Laberge JM, Puligandla P, Flageole H.
Asymptomatic congenital lung malformations.
Semin Pediatr Surg
14:16-33.
Number of Cases: 0
Focus Categories: lung cyst  cyst management  general PPB-related topic 
2005 Van Maerken T, Van Roy N, Dhooge C, Vandesompele J, Laureys G, Benoit Y, de Paepe A, Speleman F.
Cytogenetic characterization of two pleuropulmonary blastoma cases: evidence for polysomy 8, 17p loss and distal 10q loss as recurrent aberrations [Abstract].
Pediatr Blood Cancer
45(4):441.
Number of Cases: 2
Focus Categories: molecular studies 
2005 Rypens F, Garel L.
Pulmonary blastoma and multicystic nephroma: 2 cases [Abstract].
Pediatr Radiol
35(S2):S110-11.
Number of Cases: 2
Focus Categories: cystic nephroma 
2005 Piastra M, Ruggiero A, Caresta E, Granone P, Chiaretti A, Polidori G, Riccardi R.
Critical presentation of pleuropulmonary blastoma.
Pediatr Surg Int
21(3):223-6.
Number of Cases: 2
Focus Categories: lung cyst 
2005 Boman F, Hill DA, Williams GM, Bouron-Dal Soglio D, Fournet JC, Messinger Y, Priest JR.
Association of pleuropulmonary blastoma with cystic nephroma and other renal lesions: cases from the International Pleuropulmonary Blastoma Registry [Abstract].
Annual Mtg Society for Pediatr Pathol
58:84.
Number of Cases: 18
Focus Categories: Registry publication  cystic nephroma 
2005 Kim VN.
MicroRNA biogenesis: coordinated cropping and dicing.
Nature
6(5):376-85.
Number of Cases: 0
Focus Categories: DICER1 mutation 
2004 Messinger YH, Dehner LP, Hill DA, Williams G, Priest JR.
Pleuropulmonary blastoma and its association with other childhood neoplasms [abstract].
J Clin Oncol
22(14S):8542
Number of Cases: 82
Focus Categories: cystic nephroma  familial/constitutional  Registry publication 
2004 Ozer E, Sanli A, Erbayraktar S, Ulukus C, Onen A.
Congenital cystic adenomatoid malformation type 4 and aneurysm of the vein of galen: a rare coincidence or possibly related association.
Pediatr Dev Pathol
7:268-272.
Number of Cases: 1
Focus Categories: Type I PPB  familial/constitutional 
2004 Pham TT, Benirschke K, Masliah E, Stocker JT, Yi ES.
Congenital pulmonary airway malformation (congenital cystic adenomatoid malformation) with multiple extrapulmonary anomalies: autopsy report of a fetus at 19 weeks of gestation.
Pediatr Dev Pathol
7(6):661-6.
Number of Cases: 1
Focus Categories: lung cyst  general PPB-related topic  cystic nephroma 
2004 Canizares CV, Barreras PV, Aguiar RS, Diaz AP.
Blastoma pleuropulmonar en la infancia. Presentacion de un caso de dificil manejo.
Rev Cubana Pediatr
76(2): Online version.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2004 Cardinalli IAC, Okamura HO, Paiva VPP, Aguiar SA, Brandalise SRB.
Pleuropulmonary blastoma in childhood [Abstract].
Intercontinental Congress of Pathology

Number of Cases: 1
Focus Categories: lung cyst 
2004 Dosios T, Stinios J, Nicolaides P, Spyrakos S, Androulakakis E, Constantopoulos A.
Pleuropulmonary blastoma in childhood. A malignant degeneration of pulmonary cysts.
Pediatr Surg Int
20:863-5.
Number of Cases: 2
Focus Categories: cyst management  lung cyst 
2004 Hill DA, Dehner LP.
A cautionary note about congenital cystic adenomatoid malformation (CCAM) type 4 [Letter].
Am J Surg Pathol
28(4):554-5.
Number of Cases: 0
Focus Categories: cyst management  lung cyst  pathology discussion  Registry publication 
2004 Priest J, Williams G.
Incidence, timing, and outcome of central nervous system metastasis in pleuropulmonary blastoma [Abstract].
11th International Symposium on Pediatric Neuro-Oncology
EPI30:67.
Number of Cases: 24
Focus Categories: CNS metastasis  Registry publication  survival of CNS metastasis 
2004 Hasiotou M, Polyviou P, Strantzia CM, Pourtsidis A, Stinios I.
Pleuropulmonary blastoma in the area of a previously diagnosed congenital lung cyst: report of two cases.
Acta Radiol
45:289-292.
Number of Cases: 2
Focus Categories: lung cyst 
2004 Hayes-Jordan AA, Daw NC, Furman WL, Hoffer FA, Shochat SJ.
Tumor recurrence at thoracostomy tube insertion sites: a report of two pediatric cases.
J Ped Surg
39(10):1565-67.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2004 Tan Kendrick A.
Cerebral metastasis proven 1 year after an embolic cerebral infarct from pleuropulmonary blastoma [Letter to the Editor].
Pediatr Radiol
34 (3): 283.
Number of Cases: 1
Focus Categories: macrovascular invasion/embolism  CNS metastasis 
2004 MacSweeney F, Papagiannopoulos K, Goldstraw P, Sheppard MN, Corrin B, Nicholson AG.
A cautionary note about congenital cystic adenomatoid malformation (CCAM) type 4 [Reply].
Am J Surg Pathol
28(4):555.
Number of Cases: 0
Focus Categories: cyst management  lung cyst  pathology discussion 
2004 Roque L, Rodrigues R, Martins C, Ribeiro C, Ribeiro MJ, Martins AG, Oliveira P, Fonseca I.
Comparative genomic hybridization analysis of a pleuropulmonary blastoma.
Cancer Genet Cytogenet
149:58-62.
Number of Cases: 1
Focus Categories: molecular studies 
2004 Teklali Y, Kaddouri N, Benhmamouch MN, Abdelhak M, Barahioul M.
Management of pneumoblastoma in child: a case report.
Case Rep Clin Pract Rev
5:133-6.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2004 Priest J, Watterson J, Dehner L, Friend S, McIntyre J, Strong L, Hansen M, Byrd B, Feusner J, Amylon M, Bostrom B, Langston C, Pappo A.
Childhood pleuropulmonary blastoma (PPB) as a unique marker for familial childhood neoplasms [Abstract].
Proceedings of ASCO
13:186.
Number of Cases: 12
Focus Categories: Registry publication  familial/constitutional  cytogenetics 
2004 Zabolinejad N, Mir-Afsharieh SA, Afshan AB, Badiee Z.
Pleuropulmonary blastoma: case report.
Tanaffos
3(11),71-6.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2004 Quero-Hernandez A, Hernandez-Arriola J, Socorro-Lopez Z, Perez-Bautista A.
Blastoma pleuropulmonar.
Bol Med Hosp Infant Mex
61(1):55-9.
Number of Cases: 1
Focus Categories: imaging of PPB 
2004 Yamagishi M, Shuntoh K, Matsushita T, Takahashi A, Fujiwara K, Shinkawa T, Miyazaki T, Kiramura N, Toda S.
Autotransplantation and concomitant pneuectomy for an intracardiac metastatic lesion and primary pulmonary blastoma of the left lung.
Jpn J Cardiovasc Surg
33:38-41.
Number of Cases: 1
Focus Categories: macrovascular invasion/embolism 
2004 Asai T Aoyama K. Iwamura Y, Nakahara Y, Katayama S, Higashida M, Komura H, Kawasaki K, Irei K.
A case of pleuropulmonary blastoma.
Jpn J Pediatr Oncol
41(1):124-9.
Number of Cases: 1
Focus Categories: ASCR - PBSCT 
2004 Dehner LP, Tazelaar HD, Manabe T.
Pleuropulmonary blastoma.In Travis WD, Brambilla E, Muller-Hermelink HK, Harris CC (eds):
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of the Lung, Pleura, Thymus and Heart.
Lyon, IARC Press :99-100.
Number of Cases: 0
Focus Categories: general PPB-related topic  pathology discussion  Registry publication 
2003 Casey MC, Rafferty D, O'Neill M.
An unusual cause of respiratory symptoms in a toddler.
Br J Radiol
76(912): 921-2.
Number of Cases: 1
Focus Categories: imaging of PPB 
2003 Cizmar A, Kaiserova E, Kirnak J, Siman J, Plank L, Szepe P, Martanovic P, Lisy M.
Pleuropulmonary blastoma [Abstract].
8th Danube Symposium of Paediatric Surgery
287
Number of Cases: 1
Focus Categories: CNS metastasis  lung cyst 
2003 de Castro CG, de Almeida SG, Gregianin LJ, Loss JF, Rivero LF, Schwartsmann G, Brunetto AL.
High-dose chemotherapy and autologous peripheral blood stem cell rescue in a patient with pleuropulmonary blastoma.
J Pediatr Hematol Oncol
25(1): 78-81.
Number of Cases: 1
Focus Categories: ASCR - PBSCT  neo-adjuvant chemotherapy 
2003 Hong B, Chen Z, Coffin CM, Lemons R, Issa B, Brothman A, Zhou H.
Molecular cytogenetic analysis of a pleuropulmonary blastoma.
Cancer Genet Cytogenet
142:65-9.
Number of Cases: 1
Focus Categories: cytogenetics  molecular studies 
2003 Tan Kendrick AP, Krishnamurthy G, Joseph VT.
Pleuropulmonary blastoma with a large embolic cerebral infarct.
Pediatr Radiol
33:506-8.
Number of Cases: 1
Focus Categories: macrovascular invasion/embolism  CNS metastasis 
2003 MacSweeney F, Papagiannopoulos K, Goldstraw P, Sheppard MN, Corrin B, Nicholson AG.
An assessment of the expanded classification of congenital cystic adenomatoid malformations and their relationship to malignant transformation.
Am J Surg Pathol
27(8):1139-46.
Number of Cases: 1
Focus Categories: pathology discussion  major review  lung cyst  cyst management 
2003 Regragui A, Cherradi N, Sefiani S, Malihy A, Khattab M, Alhamany Z.
Blastome pleuropulmonaire: interet possible d'une chimiotherapie neoadjuvante.
Rev Pneumol Clin
59(6):365-370.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2003 Shehata BM, Abramowsky CR, Parker P, Schemankewitz E, Covinsky M, Perry A, Dehner L, Stocker JT.
Pleuropulmonary blastoma (PPB) proliferation index (MiB I) p-53, EWS fusion gene (Fli-1) expression [Abstract].
Modern Pathol
38:7P.
Number of Cases: 4
Focus Categories: molecular studies 
2003 Teeratakulpisarn J, Srinakarin J, Jintakanon D, Wiangnon S, Kuptarnond C.
Pleuropulmonary blastoma in a child presenting with spontaneous pneumothorax.
J Med Assoc Thai
86: 385-91.
Number of Cases: 1
Focus Categories: imaging of PPB 
2003 Iqbal Y, Al-Sudairy R, Abdullah FM, Al-Omari A.
Lung mass in a child.
J Pediatr Hematol Oncol
25(8):677-8.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2003 Yoruk A, Yukselgungor H.
Chemotherapy induced transverse leukonychia in children.
Intl J Dermatol
42:468-9.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2003 Langston C.
New concepts in the pathology of congenital lung malformations.
Semin Pediatr Surg
12(1):17-37.
Number of Cases: 0
Focus Categories: major review  pathology discussion 
2003 Truong LD, Choi YJ, Shen SS, Ayala G, Amato R, Krishnan B.
Renal cystic neoplasms and renal neoplasms associated with cystic renal diseases: pathogenetic and molecular links.
Adv Anat Pathol
10(3):135-159.
Number of Cases: 0
Focus Categories: cystic nephroma 
2003 Teklali Y, Kaddouri N, Afifi A, Abdelhak M, Benhmamouch N, Alaoui FM, Barahioui M.
Le Pneumoblastome chez l enfant: a propos de 6 cas.
Medecine du Maghreb
n104; Mars 2003;39-43.
Number of Cases: 6
Focus Categories: CNS metastasis 
2003 Park J, Han J, Koo H, Kim J.
Multimodal treatment of pleuropulmonary blastoma.
Korean J Thorac Cardiovasc Surg
36(8):614-8.
Number of Cases: 2
Focus Categories: general PPB-related topic  neo-adjuvant chemotherapy 
2003 Chuang PT, McMahon AP.
Branching morphogenesis of the lung: new molecular insights into an old problem.
Trends Cell Biol
13(2):86-91
Number of Cases: 0
Focus Categories: DICER1 mutation  general PPB-related topic 
2003 Chauke RF, Muthuphei MN
Pleuropulmonary blastoma - case report of a patient presenting in a moribund state.
S Afr J Surg
41(4):92-4.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2002 Kotiloglu E, Kaya H, Kiyan G, Tuney D, Canpolat C.
A rare primary pulmonary tumor of childhood.
Turk J Pediatr
44:156-9.
Number of Cases: 1
Focus Categories: bilateral  lung cyst  macrovascular invasion/embolism  neo-adjuvant chemotherapy  SVC syndrome  type progression 
2002 Kusafuka T, Kuroda S, Inoue M, Ara T, Yoneda A, Oue T, Udatsu Y, Osugi Y, Okada A.
p53 gene mutations in pleuropulmonary blastomas.
Pediatr Hematol Oncol
19(2):117-28.
Number of Cases: 3
Focus Categories: ASCR - PBSCT  CNS metastasis  cyst management  lung cyst  molecular studies  neo-adjuvant chemotherapy 
2002 Papagiannopoulos K, Hughes S, Nicholson AG, Goldstraw P.
Cystic lung lesions in the pediatric and adult population: surgical experience at the Brompton Hospital.
Ann Thorac Surg
73(5):1594-8.
Number of Cases: 1
Focus Categories: bilateral  lung cyst 
2002 Sebire NJ, Rampling D, Malone M, Ramsay A, Sheppard M.
Gains of chromosome 8 in pleuropulmonary blastomas of childhood [Letter to the Editor].
Pediatr Dev Pathol
5(2):221-2.
Number of Cases: 4
Focus Categories: cytogenetics 
2002 Stocker JT.
Congenital pulmonary airway malformation - a new name for and an expanded classification of congenital cystic adenomatoid malformation of the lung.
Histopathology
41(S2):424-31.
Number of Cases: 0
Focus Categories: pathology discussion  major review  lung cyst  general PPB-related topic 
2002 Essary LR, Vargas SO, Fletcher CDM.
Primary pleuropulmonary synovial sarcoma.
Cancer
94(2):459-69.
Number of Cases: 0
Focus Categories: general PPB-related topic  pathology discussion 
2002 Iqbal Y, Abdullah MF, Al-Jadaan SA, Trabichi H, Omari AA, Al-Sudairy R.
Embryonal rhabdomyosarcoma of the lung in a child: case report and literature review.
Annuals of Saudi Medicine
22(1-2):91-3.
Number of Cases: 1
Focus Categories: imaging of PPB 
2001 Elorriaga K, Elizalde J, Lopez Ji, Bilbao FJ.
Blastoma pleuropulmonar. A proposito de un caso [abstract].
IV Congreso Virtual Hispano Americano de Anatomia Patologica.
IV-CVHAP:Poster-E-004.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2001 Federici S, Domenichelli V, Tani G, Sciutti R, Burnelli R, Zanetti G, Domini R.
Pleuropulmonary blastoma in congenital cystic adenomatoid malformation: report of a case.
Eur J Pediatr Surg
11(3):196-9.
Number of Cases: 1
Focus Categories: cyst management  lung cyst 
2001 Granata C, Gambini C, Carlini C, Pepetto P, Torre M, Mazzola C, Mattioli G, Jasonni V.
Pleuropulmonary blastoma.
Eur J Pediatr Surg
11(4):271-3.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2001 Guler E, Tezer Kutluk M, Valcin B, Cila A, Kale G, Buyukpamukcu M.
Pleuropulmonary blastoma in a child presenting with pneumothorax.
Tumori
87: 340-2.
Number of Cases: 1
Focus Categories: lung cyst 
2001 Ishikawa N, Sato H, Tsunezuka Y, Hiranuma C, Ueno Y, Kurumaya H.
Pulmonary blastoma in a child: report of a case.
Surg Today
31:705-7.
Number of Cases: 1
Focus Categories: general PPB-related topic 
2001 Kuzucu A, Soysal O, Yakinci C, Aydin NE.
Pleuropulmonary blastoma: report of a case presenting with spontaneous pneumothorax.
Eur J Cardiothorac Surg
19(2):229-30.
Number of Cases: 1
Focus Categories: lung cyst 
2001 Leung JLY, Tsao JPY, Lai AKH, Fan TW, Chan SCH.
Pleuropulmonary blastoma in an infant presenting with tension pneumothorax.
J HK Coll Radiol
4: 219-21.
Number of Cases: 1
Focus Categories: lung cyst 
2001 Markman M.
Intraperitoneal chemotherapy in the management of malignant disease.
Expert Rev Anticancer Ther
1(1): 142-8.
Number of Cases: 0
Focus Categories: general PPB-related topic  major review 
2001 Mott BD, Canver CC, Nazeer T, Buchan A, Ilves R.
Staged resection of bilateral pleuropulmonary blastoma in a two-month old girl.
J Cardiovasc Surg
42(1):135-7.
Number of Cases: 1
Focus Categories: bilateral  cyst management  lung cyst 
2001 Nag S, Tippin D, Ruymann FB.
Intraoperative high-dose-rate brachytherapy for the treatment of pediatric tumors: the Ohio State University experience.
Int J Radiat Biol Phys
51(3):729-35.
Number of Cases: 2
Focus Categories: general PPB-related topic 
2001 Ozcan C, Celik A, Ural Z, Veral A, Kandiloglu G, Balik E.
Primary pulmonary rhabdomyosarcoma arising within cystic adenomatoid malformation: a case report and review of the literature.
J Pediatr Surg
36(7):1062-5.
Number of Cases: 1
Focus Categories: lung cyst 
2001 Papagiannopoulos KA, Sheppard M, Bush AP, Goldstraw P.
Pleuropulmonary blastoma: is prophylactic resection of congenital lung cysts effective?
Ann Thorac Surg
72(2):604-5.
Number of Cases: 1
Focus Categories: bilateral  cyst management  lung cyst 
2001 Parsons SK, Fishman SJ, Hoorntje LE, Jaramillo D, Marcus KC, Perez-Atayde AR, Kozakewich HP, Grier HE, Shamberger RC.
Aggressive multimodal treatment of pleuropulmonary blastoma.
Ann Thorac Surg
72:939-42.
Number of Cases: 2
Focus Categories: fine needle aspiration  neo-adjuvant chemotherapy 
2001 Perdikogianni C, Stiakaki E, Danilatou V, Delides G, Kalmanti M.
Pleuropulmonary blastoma: an aggressive intrathoracic neoplasm of childhood.
Pediatr Hematol Oncol
18(4):259-66.
Number of Cases: 1
Focus Categories: CNS metastasis 
2001 Shin BK, Kim MK, Park SH, Kim CY, Cho SJ, Lee KC, Kim KT, Oh YH, Kim I, Kim HK.
Fine-needle aspiration cytology of pleuropulmonary blastoma: a case report with unusual features.
Diagn Cytopathol
25(6):397-402.
Number of Cases: 1
Focus Categories: fine needle aspiration 
2001 Vargas SO, Nose V, Fletcher JA, Perez-Atayde AR.
Gains of chromosome 8 are confined to mesenchymal components in pleuropulmonary blastoma.
Pediatr Dev Pathol
4:434-45.
Number of Cases: 2
Focus Categories: cytogenetics  neo-adjuvant chemotherapy 
2001 Zeng Q, Zhou C, He Y.
Pleuropulmonary blastoma in children.
Chin J Thorac Cardiovasc Surg
17(6): 343-5.
Number of Cases: 22
Focus Categories: CNS metastasis 
2001 Roh MS, Seo JY, Huh GY, Choi PJ, Hong SH, Jeong JS.
Imprint cytologic feature of pleuropulmonary blastoma.
Korean J Cytopathol
12(1):39-43.
Number of Cases: 1
Focus Categories: lung cyst 
2001 Inoue M, Oue K, Kubota A, Kawa K.
Double megatherapy for pleuropulmonary blastoma: experience of two cases [Abstract].
Med Pediatr Oncol
37(3):267.
Number of Cases: 2
Focus Categories: ASCR - PBSCT 
2000 Barnard M, Bayani J, Grant R, Teshima I, Thorner P, Squire J.
Use of multicolor spectral karyotyping in genetic analysis of pleuropulmonary blastoma.
Pediatr Dev Pathol
3(5):479-86.
Number of Cases: 1
Focus Categories: cytogenetics 
2000 Drebov R, Brankov O, Mikhaylova V, Kamenova M, Christozova I.
Pleuropulmonary blastoma in children: diagnosis, surgical and complex treatment.
Khirurgiia
56:12-5.
Number of Cases: 10
Focus Categories: major review 
2000 Indolfi P, Casale F, Carli M, Bisogno G, Ninfo V, Cecchetto G, Bagnulo S, Santoro N, Giuliano M, Di Tullio MT.
Pleuropulmonary blastoma: management and prognosis of 11 cases.
Cancer
89(6):1396-1401.
Number of Cases: 11
Focus Categories: CNS metastasis  major review  neo-adjuvant chemotherapy 
2000 Kukkady A, Upadhyay V, Pease PW/B, Chan YF.
Pleuropulmonary blastoma: four cases.
Pediatr Surg Int
16(8):595-8.
Number of Cases: 4
Focus Categories: cyst management  cytogenetics  lung cyst 
2000 Martinez-Flores JG, Ruiz-Torres JM, Azpilcueta J, Polania-Fierro LE, Hernandez-Castillo E.
Blastoma pleuropulmonar bilateral. Informe de un caso.
Medicina Universitaria
3(9): 305-8.
Number of Cases: 1
Focus Categories: bilateral  familial/constitutional 
2000 Nicol KK, Geisinger KR.
The cytomorphology of pleuropulmonary blastoma.
Arch Pathol Lab Med
124(3):416-8.
Number of Cases: 1
Focus Categories: cyst management  fine needle aspiration  lung cyst 
2000 Picaud JC, Levrey H, Bouvier R, Chappuis JP, Louis D, Frappaz D, Claris O, Bellon G.
Bilateral cystic pleuropulmonary blastoma in early infancy.
J Pediatr
136(6):834-6
Number of Cases: 2
Focus Categories: bilateral  cyst management  familial/constitutional  lung cyst 
2000 Reix P, Levrey H, Parret M, Louis D, Bellon G.
Images pulmonaires kystiques revelatrices d'un pleuropneumoblastome.
Arch Pediatr
7:287-9.
Number of Cases: 1
Focus Categories: bilateral  cyst management 
2000 Wright JR Jr.
Pleuropulmonary blastoma. A case report documenting transition from type I (cystic) to type III (solid).
Cancer
88(12):2853-8.
Number of Cases: 1
Focus Categories: cyst management  lung cyst  type progression 
2000 Knudson AG.
Commentary: On a new genetic syndrome [Letter to the Editor].
Med & Pediatr Oncol
35:428.
Number of Cases: 0
Focus Categories: familial/constitutional  general PPB-related topic 
2000 Ishida Y, Kato K, Kigasawa H, Ohama Y, Ijiri R, Tanaka Y.
Synchronous occurrence of pleuropulmonary blastoma and cystic nephroma: possible genetic link in cystic lesions of the lung and the kidney.
Med Pediatr Oncol
35(1):85-7.
Number of Cases: 1
Focus Categories: general PPB-related topic  familial/constitutional  cystic nephroma  neo-adjuvant chemotherapy 
2000 Chan JK.
Pleuropulmonary blastoma type I, specimen partially deroofed and photographed under water.
Int J Surg Pathol
8(3):240
Number of Cases: 1
Focus Categories: Type I PPB 
2000 Vujanic GM, Jenney MEM, Adams H, Meyrick SM.
Juxtaposed cystic nephroma and Wilms’ tumor.
Pediatr Dev Pathol
3:91-4.
Number of Cases: 1
Focus Categories: pathology discussion  cystic nephroma 
1999 Baraniya J, Desai S, Kane S, Kurkure P, Nair C, Deshpande R, Borges A.
Pleuropulmonary blastoma.
Med Pediatr Oncol
32:52-6.
Number of Cases: 1
Focus Categories: neo-adjuvant chemotherapy 
1999 Benouachane T, el Khorassani M, Nachef MN, Khattab M, Alhamany Z, Barahioui M, Msefer Alaoui F.
Pleuro-pulmonary blastoma. Report of 4 cases.
Rev Mal Respir
16(3):390-4.
Number of Cases: 4
Focus Categories: general PPB-related topic 
1999 Di Tullio MT, Indolfi P, Casale F, Pettinato G, Martone A, Morgera C.
Pleuropulmonary blastoma: survival after intraocular recurrence.
Med Pediatr Oncol
33(6):588-90.
Number of Cases: 1
Focus Categories: neo-adjuvant chemotherapy  survival of CNS metastasis 
1999 Hill DA, Sadeghi S, Schultz MZ, Burr JS, Dehner LP.
Pleuropulmonary blastoma in an adult.
Cancer
85(11):2368-74.
Number of Cases: 1
Focus Categories: adult  neo-adjuvant chemotherapy  Registry publication 
1999 Huh J, Noh CI, Kim YW, Choi JY, Yun YS, Shin HY, Ahn HS, Kim YJ.
Secondary cardiac tumor in children.
Pediatr Cardiol
20:400-3.
Number of Cases: 1
Focus Categories: macrovascular invasion/embolism  SVC syndrome 
1999 Karnak I, Ciftci AO, Senocak ME, Kale G, Buyukpamukcu N.
Pulmonary blastoma: diagnostic and therapeutic aspects.
Pediatr Surg Int
15:380-82.
Number of Cases: 1
Focus Categories: general PPB-related topic 
1999 Koseoglu V, Zeybek C, Kurekci AE, Yildiz FR, Ozcan O.
Pleuropulmonary blastoma in a child.
Pediatr Int
41(2):195-7.
Number of Cases: 1
Focus Categories: general PPB-related topic 
1999 Lallier M, Bouchard S, Di Lorenzo M, Youssef S, Blanchard H, Lapierre JG, Vischoff D, Tucci M, Brochu P.
Pleuropulmonary blastoma: a rare pathology with an even rarer presentation.
J Pediatr Surg
34(7):1057-9.
Number of Cases: 1
Focus Categories: bilateral  cystic nephroma  familial/constitutional  lung cyst 
1999 Pinter A, Kalman A, Karsza L, Verebely T, Szemledy F.
Long-term outcome of congenital cystic adenomatoid malformation.
Pediatr Surg Int
15(5-6):332-5.
Number of Cases: 0
Focus Categories: lung cyst  general PPB-related topic 
1999 Romeo C, Impellizzeri P, Grosso M, Vitarelli E, Gentile C.
Pleuropulmonary blastoma: long-term survival and literature review.
Med Pediatr Oncol
33(4):372-6.
Number of Cases: 1
Focus Categories: cyst management 
1999 Rygl M, Snajdauf J, Pycha K, Kodet R, Chanova M, Hribal Z.
Primary pulmonary tumours in childhood.
Rozhl Chir
78(10):511-14.
Number of Cases: 3
Focus Categories: general PPB-related topic 
1999 Ficcardi J, Drago G, Casas E, Oliva J.
Tumores malignos pleuropulmonares primitivos de la infancia.
Rev de Cir Infantil
9(1):34-40.
Number of Cases: 2
Focus Categories: bilateral  CNS metastasis 
1999 Aubin P, Vischoff D, Haig M, Villeneuve E, Charest J, Lallier M, Di Lorenzo M.
Management of an infant with duffuse bulbous pulmonary lesions using high-frequency oscillatory ventilation.
Can J Anesth
46(10):970-4.
Number of Cases: 1
Focus Categories: cyst management  lung cyst 
1998 Drut R, Pollono D.
Pleuropulmonary blastoma: diagnosis by fine-needle aspiration cytology: a case report.
Diagn Cytopathol
19(4):303-5.
Number of Cases: 1
Focus Categories: bilateral  fine needle aspiration 
1998 Kaslovsky RA.
Concerning CCAM in children [Letter to the Editor].
Pediatr Pulmonol
26(3):230.
Number of Cases: 1
Focus Categories: lung cyst 
1998 Wyttenbach R, Vock P, Tschappeler H.
Cross-sectional imaging with CT and/or MRI of pediatric chest tumors.
Eur Radiol
8:1040-46.
Number of Cases: 1
Focus Categories: imaging of PPB 
1998 Yusuf U, Dufour D, Jenrette JM 3rd, Abboud MR, Laver J, Barredo JC.
Survival with combined modality therapy after intracerebral recurrence of pleuropulmonary blastoma.
Med Pediatr Oncol
30(1):63-6.
Number of Cases: 1
Focus Categories: bilateral  CNS metastasis  lung cyst 
1998 Gluer S, Zense M, vonSchweinitz D.
Cell adhesion molecules and intermediate filaments on embryonal childhood tumors.
Pathol Res Pract
194:773-80
Number of Cases: 1
Focus Categories: general PPB-related topic 
1998 McDermott MB, Ponder TB, Dehner LP.
Nasal chondromesenchymal hamartoma: an upper respiratory tract analogue of the chest wall mesenchymal hamartoma.
Am J Surg Pathol
22(4):425-33.
Number of Cases: 1
Focus Categories: Registry publication  pathology discussion  major review  general PPB-related topic 
1997 Priest JR, McDermott MB, Bhatia S, Watterson J, Manivel JC, Dehner LP.
Pleuropulmonary blastoma: a clinicopathologic study of 50 cases.
Cancer
80(1):147-61.
Number of Cases: 50
Focus Categories: Registry publication  major review  cyst management  bilateral 
1997 Baez-Giangreco A, Afzal M, Hamdy MG, Antonious J.
Pleuropulmonary blastoma of the lung presenting as posterior mediastinal mass: a case report.
Pediatr Hematol Oncol
14(5):475-81.
Number of Cases: 1
Focus Categories: fine needle aspiration 
1997 d'Agostino S, Bonoldi E, Dante S, Meli S, Cappellari F, Musi L.
Embryonal rhabdomyosarcoma of the lung arising in cystic adenomatoid malformation: case report and review of the literature.
J Pediatr Surg
32(9):1381-3.
Number of Cases: 1
Focus Categories: lung cyst 
1997 Adirim TA, King R, Klein BL.
Radiological case of the month.
Arch Pediatr Adolesc Med
151(10):1053-4.
Number of Cases: 1
Focus Categories: imaging of PPB  lung cyst 
1997 Gelven PL, Hopkins MA, Green CA, Harley RA, Wilson MM.
Fine-needle aspiration cytology of pleuropulmonary blastoma: case report and review of the literature.
Diagn Cytopathol
16(4):336-40.
Number of Cases: 1
Focus Categories: bilateral  fine needle aspiration  lung cyst 
1997 Kager L, Amann G, Zoubek A, Huemer C, Ambros PF, Ambros IM, Wiesbauer P, Horcher E, Hawliczek R, Gadner H.
Pleuropulmonales blastom.
Monatsschr Kinderheilkd
145:510-4.
Number of Cases: 2
Focus Categories: general PPB-related topic 
1997 Kelsey AM, McNally K, Birch J, Mitchell ELD.
Case of extra pulmonary, pleuro-pulmonary blastoma in a child: pathological and cytogenetic findings.
Med Pediatr Oncol
29:61-4.
Number of Cases: 1
Focus Categories: cytogenetics 
1997 Novak R, Dasu S, Agamanolis D, Herold W, Malone J, Waterson J.
Trisomy 8 is a characteristic finding in pleuropulmonary blastoma.
Pediatr Pathol Lab Med
17(1):99-103.
Number of Cases: 3
Focus Categories: CNS metastasis  cytogenetics 
1997 Pistevou-Gompaki K, Gompakis N, Trachana M, Kostopoulou E, Koliouskas DE.
Bad-risk childhood pleuropulmonary blastoma: does chemoradiotherapy help? [Letter to the Editor].
Med Pediatr Oncol
29(3):236.
Number of Cases: 1
Focus Categories: fine needle aspiration 
1997 Yang P, Hasegawa T, Hirose T, Fukumoto T, Uyama T, Monden Y, Sano T.
Pleuropulmonary blastoma: fluorescence in situ hybridization analysis indicating trisomy 2.
Am J Surg Pathol
21(7):854-9.
Number of Cases: 1
Focus Categories: cytogenetics 
1997 Namouni F, Tabone MD, Boccon Gibod L, Van Den Akker J, Baculard A, Gruner M, Leverger G.
Pneumoblastome developpe sur un hamartome kystique mesenchymateux du poumon [Abstract].
Arch Pediatr
4(5):496.
Number of Cases: 1
Focus Categories: general PPB-related topic 
1996 Bongo S, Coze C, Scheiner C, Coquet M, Devred P, Bernard JL.
Pneumoblastome chez l'enfant. Cas clinique et revue de la litterature.
Bull Cancer
83:877-81.
Number of Cases: 1
Focus Categories: ASCR - PBSCT 
1996 Dobard GF, Hedlund GL, Johnson WH Jr, Kelly DR, Howard TH.
Pleuropulmonary blastoma with vascular invasion.
Am J Roentgenol
166(2):308.
Number of Cases: 1
Focus Categories: macrovascular invasion/embolism  SVC syndrome 
1996 Lopez-Andreu JA, Ferris-Tortajada J, Gomez J.
Pleuropulmonary blastoma and congenital cystic malformations [Letter].
J Peds
129(5):773-5.
Number of Cases: 0
Focus Categories: lung cyst  cyst management 
1996 McDermott MB, Dehner LP, Priest JR.
Pleuropulmonary blastoma and congenital cystic malformations [Letter to the editor].
J Peds
129(5): 774-5.
Number of Cases: 0
Focus Categories: cyst management  pathology discussion  Registry publication 
1996 Merriman TE, Beasley SW, Chow CW, Smith PJ, Robertson CF.
A rare tumor masquerading as an empyema: pleuropulmonary blastoma.
Pediatr Pulmonol
22(6):408-11.
Number of Cases: 1
Focus Categories: general PPB-related topic 
1996 Priest JR, Watterson J, Strong L, Huff V, Woods WG, Byrd RL, Friend SH, Newsham I, Amylon MD, Pappo A, Mahoney DH, Langston C, Heyn R, Kohut G, Freyer DR, Bostrom B, Richardson MS, Barredo J, Dehner LP.
Pleuropulmonary blastoma: a marker for familial disease.
J Pediatr
128(2):220-4.
Number of Cases: 12
Focus Categories: Registry publication  major review  familial/constitutional  cytogenetics  cystic nephroma 
1996 Schiavetti A, Dominici C, Matrunola M, Capocaccia P, Ceccamea A, Castello MA.
Primary pulmonary rhabdomyosarcoma in childhood: clinico-biologic features in two cases with review of the literature.
Med Pediatr Oncol
26:201-7.
Number of Cases: 2
Focus Categories: CNS metastasis 
1996 Tagge EP, Mulvihill D, Chandler JC, Richardson M, Uflacker R, Othersen HB.
Childhood pleuropulmonary blastoma: caution against nonoperative management of congenital lung cysts.
J Pediatr Surg
31(1):187-90.
Number of Cases: 1
Focus Categories: bilateral  cyst management  lung cyst 
1996 Park HR, Sohn JH, Hong KW.
A case report of pleuropulmonary blastoma in childhood.
Korean J Pathol
30:351-4.
Number of Cases: 1
Focus Categories: lung cyst 
1996 Gonzalez J, Lopez AM, Martinez F, Pineda G, Martinez A.
Aspectos radiologicos del blastoma pulmonar en la infancia.
Radiologia
38(3):199-202.
Number of Cases: 4
Focus Categories: general PPB-related topic 
1995 Boyer MW, Moertel CL, Priest JR, Woods WG.
Use of intracavitary cisplatin for the treatment of childhood solid tumors in the chest or abdominal cavity.
J Clin Oncol
13(3):631-6.
Number of Cases: 2
Focus Categories: Registry publication 
1995 Dehner LP, Watterson J, Priest J.
Pleuropulmonary blastoma. A unique intrathoracic-pulmonary neoplasm of childhood.
Perspect Pediatr Pathol
18:214-26.
Number of Cases: 38
Focus Categories: major review  pathology discussion  Registry publication 
1995 Katz DS, Scalzetti EM, Groskin SA, Kohman LJ, Patel LS, Landas S.
Pleuropulmonary blastoma simulating an empyema in a young child.
J Thorac Imaging
10(2):112-6.
Number of Cases: 1
Focus Categories: general PPB-related topic 
1995 Richardson MS, Hazen-Martin D, Re G, Cantu E, Garvin AJ.
Pleuropulmonary blastoma: characterization of a pediatric tumor and its resulting tumor cell line [Abstract].
Mod Pathol
8:144A.
Number of Cases: 0
Focus Categories: cytogenetics 
1995 Schmaltz C, Sauter S, Opitz O, Harms D, Kremens B, Lohner M, Metz K, Brandis M, Niemeyer C.
Pleuro-pulmonary blastoma: a case report and review of the literature.
Med Pediatr Oncol
25:479-84.
Number of Cases: 1
Focus Categories: ASCR - PBSCT 
1995 Cottingham SL, Groner J, Kohut GJ, Qualman SJ.
Cystic nephroma and pulmonary mesenchymal lesions-a genetic link [Abstract].
Society for Pediatric Pathology Annual Meeting

Number of Cases: 1
Focus Categories: cystic nephroma  familial/constitutional 
1994 Dehner LP.
Pleuropulmonary blastoma is THE pulmonary blastoma of childhood.
Semin Diagn Pathol
11(2):144-51.
Number of Cases: 0
Focus Categories: major review  pathology discussion  Registry publication 
1994 Lopez-Andreu JA, Ferris J, Esquembre C, Verdeguer A, Esteban MJ, Paradis A, Costa E, Castel V.
Blastoma pulmonar pediatrico. Revision de la literatura y aportacion de un caso.
Oncologia
17(49):65-74.
Number of Cases: 1
Focus Categories: bilateral  familial/constitutional  major review 
1994 Paupe A, Martelli H, Lenclen R, Blanc P, Beydon N, Jaubert F, Flamant F, Scheinmann P, Oliver-Martin M.
Pneumothorax chez un nourrisson revelateur d'un pneumoblastome.
Arch Pediatr
1:919-22.
Number of Cases: 1
Focus Categories: general PPB-related topic 
1994 Sciot R, Dal Cin P, Brock P, Moerman P, Van Damme B, De Wever I, Casteels-Van Daele M, Van Den Berghe H, Desmet V.
Pleuropulmonary blastoma (pulmonary blastoma of childhood): genetic link with other embryonal malignancies?
Histopathology
24:559-63.
Number of Cases: 1
Focus Categories: cytogenetics 
1994 Seballos RM, Klein RL.
Pulmonary blastoma in children: report of two cases and review of literature.
J Pediatr Surg
29(12): 1553-6.
Number of Cases: 2
Focus Categories: CNS metastasis 
1993 Bogers AJJC, Hazebroek FWJ, Molenaar J, Bos E.
Surgical treatment of congenital bronchopulmonary disease in children.
Eur J Cardio-thorac Surg
7:117-120.
Number of Cases: 1
Focus Categories: cyst management  general PPB-related topic 
1993 Calabria R, Srikanth MS, Chamberlin K, Bloch J, Atkinson JB.
Management of pulmonary blastoma in children.
Am Surg
59:192-6.
Number of Cases: 5
Focus Categories: lung cyst 
1993 Delahunt B, Thomson KJ, Ferguson AF, Neale TJ, Meffan PJ, Nacey JN.
Familial cystic nephroma and pleuropulmonary blastoma.
Cancer
71(4):1338-42.
Number of Cases: 1
Focus Categories: cystic nephroma  familial/constitutional 
1993 Hachitanda Y, Aoyama C, Sato JK, Shimada H.
Pleuropulmonary blastoma in childhood. A tumor of divergent differentiation.
Am J Surg Pathol
17(4):382-91.
Number of Cases: 7
Focus Categories: pathology discussion 
1993 Howman-Giles R, Pozza LD, Uren R.
Ga-67 Scintigraphy in pulmonary blastoma in a child.
Clin Nuc Med
18(2): 120-22.
Number of Cases: 1
Focus Categories: CNS metastasis 
1993 Lopez-Andreu JA, Ferris J, Esquembre C, Verdeguer A, Gomez J, Castel V.
Familial cystic nephroma and pleuropulmonary blastoma.
Cancer
72(9):2792-3.
Number of Cases: 1
Focus Categories: bilateral  cystic nephroma  familial/constitutional  fine needle aspiration  neo-adjuvant chemotherapy 
1993 McDermott VGM, Mackenzie S, Hendry GMA.
Case report: primary intrathoracic rhabdomyosarcoma: a rare childhood malignancy.
Br J Radiol
66:937-41.
Number of Cases: 2
Focus Categories: CNS metastasis  lung cyst 
1993 Micallef-Eynaud PD, Goulden NT, Langdale-Brown B, Eden TB, Steers JW.
Intracerebral recurrence of primary intrathoracic rhabdomyosarcoma.
Med Pediatr Oncol
21:132-6.
Number of Cases: 2
Focus Categories: CNS metastasis  lung cyst  neo-adjuvant chemotherapy 
1993 Moshyedi AC, Mahmud F, Wood BP.
Radiological case of the month. Pulmonary blastoma.
Am J Dis Child
147(5):587-8.
Number of Cases: 1
Focus Categories: imaging of PPB 
1993 Rialland X, Pein F, Saint-Andre JP, Flamant F.
Translocation t(11;19) (q23;p13) in a child with myelomonocytic leukemia following 2 years after chemotherapy for pneumoblastoma
Med Pediatr Oncol
21:146-9.
Number of Cases: 1
Focus Categories: familial/constitutional 
1992 Kovanlikaya A, Pirnar T, Olgun N.
Pulmonary blastoma: a rare case of childhood malignancy.
Pediatr Radiol
;22:155.
Number of Cases: 1
Focus Categories: general PPB-related topic 
1992 Meza MP, Newman B, Dickman PS, Towbin RB.
Pediatric case of the day.
RadioGraphics
12:843-4.
Number of Cases: 1
Focus Categories: imaging of PPB 
1992 Murphy JJ, Blair GK, Fraser GC, Ashmore PG, LeBlanc JG, Sett SS, Rogers P, Magee JF, Taylor GP, Dimmick J.
Rhabdomyosarcoma arising within congenital pulmonary cysts: report of three cases.
J Pediatr Surg
27(10):1364-7.
Number of Cases: 3
Focus Categories: lung cyst 
1992 Ben Becher S, Zaafouri M, Bardi I, Ben Jaballah N, Besbes M, Kilani T, Boudhina T.
Le pneumoblastome.
Arch Fr Pediatr
49:109-12.
Number of Cases: 1
Focus Categories: CNS metastasis 
1991 Cohen M, Emms M, Kaschula RO.
Childhood pulmonary blastoma: a pleuropulmonary variant of the adult-type pulmonary blastoma.
Pediatr Pathol
11(5):737-49.
Number of Cases: 2
Focus Categories: CNS metastasis  pathology discussion 
1991 Senac MO Jr, Wood BP, Isaacs H, Weller M.
Pulmonary blastoma: a rare childhood malignancy.
Radiology
179(3):743-6.
Number of Cases: 7
Focus Categories: CNS metastasis 
1990 Cairoli G, Bertana S, Giuntoli M, Battisti C.
La malformazione adenomatoide cistica del polmone: esperienza in 4 casi operati.
Ped Med Chir
12:681-6.
Number of Cases: 1
Focus Categories: lung cyst 
1990 Domizio P, Liesner RJ, Dicks-Mireaux C, Risdon RA.
Malignant mesenchymoma associated with a congenital lung cyst in a child: case report and review of the literature.
Pediatr Pathol
10:785-97.
Number of Cases: 1
Focus Categories: lung cyst  pathology discussion 
1990 Drut R, Drut RM.
Blastoma pleuropulmonar.
Patologia
23:197-200.
Number of Cases: 1
Focus Categories: bilateral  familial/constitutional  lung cyst 
1990 Ozkaynak MF, Ortega JA, Laug W, Gilsanz V, Isaacs H.
Role of chemotherapy in pediatric pulmonary blastoma.
Med Pediatr Oncol
18:53-6.
Number of Cases: 2
Focus Categories: neo-adjuvant chemotherapy 
1989 Bove KE.
Sarcoma arising in pulmonary cystic mesenchymal hamartoma.
Pediatr Pathol
9:785-92.
Number of Cases: 1
Focus Categories: lung cyst 
1989 Hedlund GL, Bisset GS, Bove KE.
Malignant neoplasms arising in cystic hamartomas of the lung in childhood.
Radiology
173: 77-9.
Number of Cases: 2
Focus Categories: lung cyst 
1989 Joshi VV, Beckwith JB.
Multilocular cyst of the kidney (cystic nephroma) and cystic, partially differentiated nephroblastoma.
Cancer
64:466-79.
Number of Cases: 1
Focus Categories: cystic nephroma  familial/constitutional 
1989 Shimokama T, Watanabe T.
Multilocular renal cyst. Scanning and transmission electron microscopic observations.
Path Res Pract
184:255-59.
Number of Cases: 0
Focus Categories: cystic nephroma  general PPB-related topic  lung cyst 
1988 Manivel JC, Priest JR, Watterson J, Steiner M, Woods WG, Wick MR, Dehner LP.
Pleuropulmonary blastoma. The so-called pulmonary blastoma of childhood.
Cancer
62(8):1516-26.
Number of Cases: 11
Focus Categories: major review  pathology discussion  Registry publication 
1988 Shariff S, Thomas JA, Shetty N, D'Cunha S.
Primary pulmonary rhabdomyosarcoma in a child, with a review of literature.
J Surg Oncol
38:261-4.
Number of Cases: 1
Focus Categories: lung cyst 
1987 Allan BT, Day DL, Dehner LP.
Primary pulmonary rhabdomyosarcoma of the lung in children. Report of two cases presenting with spontaneous pneumothorax.
Cancer
59(5):1005-11.
Number of Cases: 2
Focus Categories: lung cyst  Registry publication 
1987 Becroft DMO, Jagusch MF.
Pulmonary sarcomas arising in mesenchymal cystic hamartomas [Abstract].
Pediatr Pathol
7(4):478.
Number of Cases: 3
Focus Categories: lung cyst 
1987 Jimenez JF.
Pulmonary blastoma in childhood.
J Surg Oncol
34:87-93.
Number of Cases: 1
Focus Categories: general PPB-related topic 
1987 Manivel C, Wick M, Dehner L.
Thoracopulmonary blastoma - reassessment of an embryonal neoplasm [Abstract].
Lab Invest
56:46A.
Number of Cases: 9
Focus Categories: pathology discussion  Registry publication 
1987 Selle B, Dorffel W, Wit J.
Das pulmonale blastom im kindesalter-eine kasuistik und eine ubersicht uber die literatur
Z Kinderchir
42(6):373-7.
Number of Cases: 1
Focus Categories: bilateral  CNS metastasis  lung cyst 
1987 Graham JM, Boyle W, Troxell J, Cullity GJ, Sprague PL, Beckwith JB.
Cystic hamartomata of lung and kidney: a spectrum of developmental abnormalities
Am J Med Genetics
27:45-59
Number of Cases: 0
Focus Categories: lung cyst  cystic nephroma  familial/constitutional  general PPB-related topic 
1986 Fisher JE, Khan AR, Jewett TC, Allen J, Afshani E.
Childhood pneumoblastoma (pulmonary blastoma) and adult chondroid hamartoma of lung--a unifying concept [Abstract].
Pediatr Pathol
5:94-95.
Number of Cases: 1
Focus Categories: lung cyst  general PPB-related topic 
1986 Mark E.
Mesenchymal cystic hamartoma of the lung.
N Engl J Med
315:1255-9.
Number of Cases: 1
Focus Categories: general PPB-related topic  pathology discussion 
1986 Morales L, Julia V, Tardio E, Cardesa A, Cruz M.
Blastome pulmonaire sur kyste pulmonaire congenital
Chir Pediatr
27(1):53-6.
Number of Cases: 1
Focus Categories: lung cyst 
1986 Williams RA.
Embryonal rhabdomyosarcoma occurring in cystic adenomatoid malformation [Abstract].
Pediatr Pathol
5:118-9.
Number of Cases: 1
Focus Categories: lung cyst 
1984 Holland-Moritz RM, Heyn RM.
Pulmonary blastoma associated with cystic lesions in children.
Med Pediatr Oncol
12(2):85-8.
Number of Cases: 1
Focus Categories: cyst management  cystic nephroma  lung cyst 
1983 Ashworth TG.
Pulmonary blastoma - a true congenital neoplasm.
Histopathol
7:585-94.
Number of Cases: 1
Focus Categories: pathology discussion 
1983 Galifer RB, Margueritte G, Gubler JP, Jean R, Pous JG.
Le pneumoblastome chez l'enfant.
Chir Pediatr
24: 187-91.
Number of Cases: 2
Focus Categories: macrovascular invasion/embolism 
1983 Ohtomo K, Araki T, Yashiro N, Iio M.
Pulmonary blastoma in children.
Radiology
147: 101-4.
Number of Cases: 2
Focus Categories: lung cyst 
1983 Takahashi A, Konda R, Satoh T, Mori T.
A case of brain metastasis of primary pulmonary rhabdomyosarcoma in a child.
No Shinkei Geka
11(3):313-20.
Number of Cases: 1
Focus Categories: CNS metastasis 
1982 Weinblatt ME, Siegel SE, Isaacs H.
Pulmonary blastoma associated with cystic lung disease.
Cancer
49(4):669-71.
Number of Cases: 1
Focus Categories: lung cyst 
1981 Krous HF, Sexauer CL.
Embryonal rhabdomyosarcoma arising within a congenital bronchogenic cyst in a child.
J Pediatr Surg
16: 506-8.
Number of Cases: 1
Focus Categories: CNS metastasis  familial/constitutional  lung cyst 
1981 Thomas WJ, Koenig HM, Ellwanger FR, Lightsey AL.
Primary pulmonary rhabdomyosarcoma in childhood.
Am J Dis Child
135:469-71.
Number of Cases: 1
Focus Categories: general PPB-related topic 
1980 Weinberg AG, Currarino G, Moore GC, Votteler TP.
Mesenchymal neoplasia and congenital pulmonary cysts.
Pediatr Radiol
9:179-82.
Number of Cases: 1
Focus Categories: lung cyst 
1979 Bove KE.
Pulmonary blastoma [Letter to the Editor].
Am J Surg Pathol
3(4):383.
Number of Cases: 1
Focus Categories: general PPB-related topic 
1979 Sumner TE, Phelps CR 2nd, Crowe JE, Poolos SP, Shaffner LD.
Pulmonary blastoma in a child.
Am J Roentgenol
133(1):147-8.
Number of Cases: 1
Focus Categories: cyst management  lung cyst 
1979 Abt AB, Demers LM, Shochat SJ.
Cystic nephroma: an ultrastructural and biochemical study.
J Urol
122:539-41.
Number of Cases: 0
Focus Categories: cystic nephroma  general PPB-related topic  lung cyst 
1978 Valderrama E, Saluja G, Shende A, Lanzkowsky P, Berkman J.
Pulmonary blastoma, report of two cases in children.
Am J Surg Pathol
2:415-22.
Number of Cases: 2
Focus Categories: lung cyst 
1978 Martinez JC, Chaves Pecero F, Gutierrez de la Pena C, Martin Gomez R, Gutierrez del Manzano JA, Flores Corral T, Loscertales Abril J.
Pulmonary blastoma: report of a case.
J Pediatr Surg
13(1):93-4.
Number of Cases: 1
Focus Categories: cyst management 
1977 Ueda K, Gruppo R, Unger F, Martin L, Bove K.
Rhabdomyosarcoma of lung arising in congenital cystic adenomaoid malformation.
Cancer
40:383-8.
Number of Cases: 1
Focus Categories: lung cyst 
1975 Pilon R.
Un cancer pulmonaire exceptionnel: le pneumoblastome.
Mediterrane Medicale
74:26-43.
Number of Cases: 1
Focus Categories: general PPB-related topic 
1964 Williams DI.
Nephroblastoma. Clinical picture and diagnosis [Fig 155, p252]. In: Riches E (Ed) Tumors of the kidney and ureter.
Riches E (Ed) Tumors of the kidney and ureter.Edinburgh & London, Livingstone.
235-54 [Fig 155, p252]
Number of Cases: 0
Focus Categories: cystic nephroma  general PPB-related topic  lung cyst 
1963 Stephanopoulos C, Catsaras H.
Myxosarcoma complicating a cystic hamartoma of the lung.
Thorax
18:144.
Number of Cases: 1
Focus Categories: lung cyst 
1962 Boss JH.
Mixed embyonic tumor of the lung in a three year old girl.
Am Rev Respir Dis
85:735-40.
Number of Cases: 1
Focus Categories: general PPB-related topic 

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