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The International Pleuropulmonary Blastoma Registry
The International Pleuropulmonary Blastoma Registry
The Genetics of PPB

Critical Issues


Constitutional & Familial Issues: Genetics of PPB:


A Very Rare Disease: Enrolling Patients in the Registry


Cerebral Metastases in PPB


Genetic Study of PPB


PPB Associated with Cystic Nephroma and Other Renal Tumors


Type I PPB: Treatment Issues


Type II and III THERAPY RECOMMENDATION CHANGE

Join Our PPB Study

Whats New

04/09/2010
2010 PPB FAMILY WEEKEND IN WASHINGTON DC

02/15/2007
THERAPY CHANGE: PPB Types II and III

11/15/2006
PPB, Cystic Nephroma & Small Bowel Polyps

10/01/2005
Genetic Study in PPB - PPB Tissue Bank

Registry Publications
The following is a list of publications and abstracts by members of the International PPB Registry, most recent first. To obtain any of these publications, please contact Gretchen Williams at 612-813-7115 or at gretchen.williams@childrensmn.org.
43 Results :
2010 Priest JR, Jaffe A.
Increasing incidence of detection of congenital lung lesions [Reply].
Pediatr Pulmonol
45:104.
2010 Hill DA, Wang JD, Schoettler P, Dehner L, Ivanovich J, Bracamontes D, Williams G, Messinger Y, Goodfellow PJ, Priest J.
Germline DICER1 mutations are common in both hereditary and presumed sporadic pleuropulmonary blastoma [Abstract].
Lab Invest
90:311
2010 Cross SF, Arbuckle S, Priest JR, Marshall G, Charles A, Dalla Pozza, L.
Familial Pleuropulmonary Blastoma in Australia
Pediatric Blood and Cancer
in press
2010 Cummings NM, Desai S, Thway K, Stewart S, Hill DA, Priest JR, Nicholson AG, Rintoul RC.
Cystic primary pulmonary synovial sarcoma presenting as recurrent pneumothorax: report of four cases.
Am J Surg Pathol
34(8):1176-79.
2010 Schultz KA, Williams G, Hill D, Dehner LP, Priest J.
Ovarian tumors in association with pleuropulmonary blastoma: a new manifestation of the PPB Tumor syndrome [Abstract].
Pediatr Blood Cancer
54(6):850
2010 Priest JR, Williams GM, Mize WA, Dehner LP.
Priest JR, Williams GM, Mize WA, Dehner LP. Nasal chondromesenchymal hamartoma in children with pleuropulmonary blastoma: a report from the International Pleuropulmonary Blastoma Registry.
Int J Pediatr Otorhinolaryngol
[in press]
2010 Priest JR, Andic D, Arbuckle S, Gonzalez-Gomez I, Hill DA Williams G.
Great vessel and cardiac extension and tumor embolism in pleuropulmonary blastoma - a report from the International Pleuropulmonary Blastoma Registry
Pediatric Blood and Cancer
in press
2009 Priest JR, Williams GM, Hill DA, Dehner LP, Jaffé A.
Pulmonary cysts in early childhood and the risk of malignancy.
Pediatr Pulmonol
44(1):14-30.
2009 Hill DA, Ivanovich J, Priest JR, Gurnett CA, Dehner LP, Desruisseau D, Jarzembowski JA, Wikenheiser KA, Suarez BK, Whelan AJ, Williams G, Bracamontes B, Messinger Y, Goodfellow PJ.
Inherited DICER1 mutations in familial pleuropulmonary blastoma [abstract].
Annual Meeting for American Association for Cancer Research
Abstract LB-91.
2009 Dehner LP.
USCAP Specialty Conference, case 4: Sertoli cell tumor of the ovary.
Pediatr Dev Pathol
In Press
2009 Hill DA, Ivanovich J, Priest JR, Gurnett CA, Dehner LP, Desruisseau D, Jarzembowski JA, Wikenheiser-Brokamp KA, Suarez BK, Whelan AJ, Williams G, Bracamontes D, Messinger Y, Goodfellow PJ.
DICER1 Mutations in Familial Pleuropulmonary Blastoma.
Science
325:965
2009 Schiavetti A, Indolfi P, Hill DA, Priest JR
Primary pulmonary rhabdomyosarcoma in childhood: clinico-biologic features in two cases with review of the literature--erratum
Pediatr Blood Cancer
52(1):146.
2008 Hill DA, Jarzembowski JA, Priest JR, Williams G, Schoettler P, Dehner LP.
Type I pleuropulmonary blastoma: pathology and biology study of 51 cases from the International Pleuropulmonary Blastoma Registry.
Am J Surg Pathol
32(2):282-295
2007 Lennerz JK, Jarzembowski JA, Spence D, Schoettler P, Dehner LP, Hill DA.
Diagnostic features of pleuropulmonary blastoma (PPB) are absent in congenital cystic adenomatoid malformation [Abstract].
Annual Meeting of the Society for Pediatric Pathology
Mar.
2007 Hill DA, Jarzembowski JA, Lennerz JK, Spence D, Schoettler P, Priest JR, Williams G, Dehner LP.
Histologic features of Type I pleuropulmonary blastoma (PPB) [Abstract].
Annual Meeting of the Society for Pediatric Pathology
Mar.
2007 Priest JR, Magnuson J, Williams GM, Abromowitch M, Byrd R, Sprinz P, Finkelstein M, Moertel CL, Hill DA.
Cerebral metastasis and other central nervous system complications of pleuropulmonary blastoma.
Pediatr Blood Cancer
49(3):266-73.
2007 Pai S, Eng HL, Lee SY, Hsaio CC, Huang WT, Huang SC, Hill DA, Dehner LP, Priest JR.
Correction: Pleuropulmonary blastoma, not rhabdomyosarcoma in a congenital lung cyst [Letter to the Editor].
Pediatr Blood Cancer
Mar;48(3):370-1.
2007 Hill DA, Dishop MK, McKay EM, Langston C, Priest JR, Dehner LP.
Immature interstitial mesenchymal tumor (IIMT): a distinctive new entity of the infant lung [Abstract].
Mod Pathol
20:279-300.
2006 Hill DA, Williams GM, Finkelstein MJ, Serrano MF, Dehner LP, Priest JR.
Significance of histologic type and anaplasia in pleuropulmonary blastoma [Abstract].
Lab Invest
86(Suppl):212-27.
2006 Priest JR, Hill DA, Williams GM, Moertel CM, Messinger Y, Finkelstein MJ, Dehner LP.
Type I pleuropulmonary blastoma: A report from the International Pleuropulmonary Blastoma Registry.
J Clin Oncol
24:4492-8.
2006 Stefanaki K, Boman F, Stassinopoulou A, Williams GM, Fournet JC, Bouron-Dal Soglio D, Chauvenet A, Hill A, Messinger Y, Priest JR.
Association of pleuropulmonary blastoma with cystic nephroma and small bowel polyp: case report and data from the International Pleuropulmonary Blastoma Registry [Abstract].
Virchows Arch
448:692.
2006 Boman F, Hill DA, Williams GM, Chauvenet A, Fournet JC, BouronDalSoglio D, Messinger Y, Priest JR.
Familial association of pleuropulmonary blastoma with cystic nephroma and other renal tumors: a report from the International Pleuropulmonary Blastoma Registry.
J Pediatr
149(6):850-4.e2.
2005 Hill DA.
USCAP Specialty Conference, case 1: Type I Pleuropulmonary blastoma.
Pediatr Dev Pathol
8:77-84
2005 Priest JR, Messinger Y, Finkelstein MJ, Williams GM, Hill DA, Dehner LP, Moertel CL.
Treatment modality vs outcome in Type I pleuropulmonary blastoma (PPB) - Results from The PPB Registry [abstract].
Pediatr Blood Cancer
44(6):544
2005 Dehner LP.
Beware of "degenerating" congenital pulmonary cysts [Letter to the Editor].
Pediatr Surg Int
21:123-4
2005 Serrano MF, Dehner LP, Williams GM, Priest JR, Hill DA.
Histologic predictors of central nervous system metastasis in pleuropulmonary blastoma: a pilot study [Abstract].
Mod Pathol
18:303.
2005 Boman F, Hill DA, Williams GM, Bouron-Dal Soglio D, Fournet JC, Messinger Y, Priest JR.
Association of pleuropulmonary blastoma with cystic nephroma and other renal lesions: cases from the International Pleuropulmonary Blastoma Registry [Abstract].
Annual Mtg Society for Pediatr Pathol
58:84.
2004 Priest J, Williams G.
Incidence, timing, and outcome of central nervous system metastasis in pleuropulmonary blastoma [Abstract].
11th International Symposium on Pediatric Neuro-Oncology
EPI30:67.
2004 Dehner LP, Tazelaar HD, Manabe T.
Pleuropulmonary blastoma.In Travis WD, Brambilla E, Muller-Hermelink HK, Harris CC (eds):
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of the Lung, Pleura, Thymus and Heart.
Lyon, IARC Press :99-100.
2004 Hill DA, Dehner LP.
A cautionary note about congenital cystic adenomatoid malformation (CCAM) type 4 [Letter].
Am J Surg Pathol
28(4):554-5.
2004 Messinger YH, Dehner LP, Hill DA, Williams G, Priest JR.
Pleuropulmonary blastoma and its association with other childhood neoplasms [abstract].
J Clin Oncol
22(14S):8542
2004 Priest J, Watterson J, Dehner L, Friend S, McIntyre J, Strong L, Hansen M, Byrd B, Feusner J, Amylon M, Bostrom B, Langston C, Pappo A.
Childhood pleuropulmonary blastoma (PPB) as a unique marker for familial childhood neoplasms [Abstract].
Proceedings of ASCO
13:186.
1999 Hill DA, Sadeghi S, Schultz MZ, Burr JS, Dehner LP.
Pleuropulmonary blastoma in an adult.
Cancer
85(11):2368-74.
1998 McDermott MB, Ponder TB, Dehner LP.
Nasal chondromesenchymal hamartoma: an upper respiratory tract analogue of the chest wall mesenchymal hamartoma.
Am J Surg Pathol
22(4):425-33.
1997 Priest JR, McDermott MB, Bhatia S, Watterson J, Manivel JC, Dehner LP.
Pleuropulmonary blastoma: a clinicopathologic study of 50 cases.
Cancer
80(1):147-61.
1996 McDermott MB, Dehner LP, Priest JR.
Pleuropulmonary blastoma and congenital cystic malformations [Letter to the editor].
J Peds
129(5): 774-5.
1996 Priest JR, Watterson J, Strong L, Huff V, Woods WG, Byrd RL, Friend SH, Newsham I, Amylon MD, Pappo A, Mahoney DH, Langston C, Heyn R, Kohut G, Freyer DR, Bostrom B, Richardson MS, Barredo J, Dehner LP.
Pleuropulmonary blastoma: a marker for familial disease.
J Pediatr
128(2):220-4.
1995 Boyer MW, Moertel CL, Priest JR, Woods WG.
Use of intracavitary cisplatin for the treatment of childhood solid tumors in the chest or abdominal cavity.
J Clin Oncol
13(3):631-6.
1995 Dehner LP, Watterson J, Priest J.
Pleuropulmonary blastoma. A unique intrathoracic-pulmonary neoplasm of childhood.
Perspect Pediatr Pathol
18:214-26.
1994 Dehner LP.
Pleuropulmonary blastoma is THE pulmonary blastoma of childhood.
Semin Diagn Pathol
11(2):144-51.
1988 Manivel JC, Priest JR, Watterson J, Steiner M, Woods WG, Wick MR, Dehner LP.
Pleuropulmonary blastoma. The so-called pulmonary blastoma of childhood.
Cancer
62(8):1516-26.
1987 Allan BT, Day DL, Dehner LP.
Primary pulmonary rhabdomyosarcoma of the lung in children. Report of two cases presenting with spontaneous pneumothorax.
Cancer
59(5):1005-11.
1987 Manivel C, Wick M, Dehner L.
Thoracopulmonary blastoma - reassessment of an embryonal neoplasm [Abstract].
Lab Invest
56:46A.




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Data and recommendations on this site are conscientiously presented but some are unpublished observations and have not undergone peer review. Consultation with the Registry is encouraged to clarify any topics. The International PPB Registry advises caution in the citation of website information.
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