The International Pleuropulmonary Blastoma Registry

	Overall	Type I	Type II	Type III
Published Registry Series N=50**
Age Range** (months)	0-147*	0-28	15-64	31-147
Median Age** (months)	38	10	34	44
Unpublished Registry Series N=128**
Age Range** (months)	0-431	0-32	6-431***	15-147
Median Age** (months)		10	36	44

These age differences by Type are statistically significant.
*The disease has rarely been reported in adults [see Bibliography, Focus: adult].
** Data from Registry publication of 50 cases [Priest,1997]

*** One 36 yr-old with documented PPB in the Registry series [see Registry Publications, Hill 1999].

Incidence histograms by Type versus Age are as follows (unpublished Registry and Bibliography cases):

Gender

males approximately equal females. Unpublished Registry data: in 138 centrally reviewed cases, there were 72 females and 66 males.

Laterality

Unpublished Registry data: in 134 centrally-reviewed Registry cases, disease was on the right side in 72 children (54%), left in 50 children (37%), and bilateral lung disease (bilateral PPB or PPB one side and lung cysts other side) in 12 children (9%).